Sfoglia per Autore
Modeling Sarcoglycanopathy in Danio rerio
2023 Dalla Barba, Francesco; Soardi, Michela; Mouhib, Leila; Risato, Giovanni; Akyürek, Eylem Emek; Lucon-Xiccato, Tyrone; Scano, Martina; Benetollo, Alberto; Sacchetto, Roberta; Richard, Isabelle; Argenton, Francesco; Bertolucci, Cristiano; Carotti, Marcello; Sandonà, Dorianna
Exploiting HOPNO-dicopper center interaction to development of inhibitors for human tyrosinase
2023 Buitrago, E.; Faure, C.; Carotti, M.; Bergantino, E.; Hardre, R.; Maresca, M.; Philouze, C.; Vanthuyne, N.; Boumendjel, A.; Bubacco, L.; du Moulinet d'Hardemare, A.; Jamet, H.; Reglier, M.; Belle, C.
Synthesis and Evaluation of Bithiazole Derivatives As Potential α-Sarcoglycan Correctors
2023 Ribaudo, Giovanni; Carotti, Marcello; Ongaro, Alberto; Oselladore, Erika; Scano, Martina; Zagotto, Giuseppe; Sandonà, Dorianna; Gianoncelli, Alessandra
C17 corrector for the treatment of sarcoglycanopathy: preliminary ADME studies
2022 Benetollo, Alberto; Scano, Martina; Parrasia, Sofia; Biasutto, Lucia; DALLA BARBA, Francesco; Caccin, Paola; Carotti, Marcello; Sandona', Dorianna
Zebrafish as a model for sarcoglycanopathies: in-depth analysis of the disease phenotype
2022 DALLA BARBA, Francesco; Soardi, Michela; Scano, Martina; Benetollo, Alberto; Carotti, Marcello; Caccin, Paola; Risato, Giovanni; Argenton, Francesco; Sandonà, Dorianna
CFTR corrector C17 is effective in muscular dystrophy, in vivo proof of concept in LGMDR3
2022 Scano, Martina; Benetollo, Alberto; Nogara, Leonardo; Bondì, Michela; DALLA BARBA, Francesco; Soardi, Michela; Furlan, Sandra; Akyurek, EYLEM EMEK; Caccin, Paola; Carotti, Marcello; Sacchetto, Roberta; Blaauw, Bert; Sandonà, Dorianna
Targeting of PFKFB3 with miR-206 but not mir-26b inhibits ovarian cancer cell proliferation and migration involving FAK downregulation
2022 Boscaro, Carlotta; Baggio, Chiara; Carotti, Marcello; Sandonà, Dorianna; Trevisi, Lucia; Cignarella, Andrea; Bolego, Chiara
Differential Analysis of Gly211Val and Gly286Val Mutations Affecting Sarco(endo)plasmic Reticulum Ca2+-ATPase (SERCA1) in Congenital Pseudomyotonia Romagnola Cattle
2022 Akyurek, Eylem Emek; Busato, Francesca; Murgiano, Leonardo; Bianchini, Elisa; Carotti, Marcello; Sandonà, Dorianna; Drögemüller, Cord; Gentile, Arcangelo; Sacchetto, Roberta
In vivo rescue of α-sarcoglycan mutants by CFTR correctors
2021 Scano, Martina; Benetollo, Alberto; Bondi', Michela; Caccin, Paola; Carotti, Marcello; DALLA BARBA, Francesco; Soardi, Michela; Sacchetto, Roberta; Sandona', Dorianna
In vivo recovery of α-sarcoglycan mutants by protein folding correctors
2021 Scano, Martina; Benetollo, Alberto; Bondi', Michela; Caccin, Paola; Carotti, Marcello; DALLA BARBA, Francesco; Soardi, Michela; Sacchetto, Roberta; Sandona', Dorianna
In vivo proof of concept of the efficacy of the CFTR corrector C17 in a sarcoglycanopathy mouse model
2021 Scano, Martina; Benetollo, Alberto; Nogara, Leonardo; Bondi', Michela; DALLA BARBA, Francesco; Caccin, Paola; Carotti, Marcello; Sacchetto, Roberta; Blaauw, Bert; Sandona', Dorianna
In vivo recovery of α-sarcoglycan mutants by protein folding correctors
2021 Scano, Martina; Benetollo, Alberto; Bondi', Michela; Caccin, Paola; Carotti, Marcello; DALLA BARBA, Francesco; Soardi, Michela; Sacchetto, Roberta; Sandona', Dorianna
Ditopic Chelators of Dicopper Centers for Enhanced Tyrosinases Inhibition
2021 Buitrago, E.; Faure, C.; Challali, L.; Bergantino, E.; Boumendjel, A.; Bubacco, L.; Carotti, M.; Hardre, R.; Maresca, M.; Philouze, C.; Jamet, H.; Reglier, M.; Belle, C.
Combined Use of CFTR Correctors in LGMD2D Myotubes Improves Sarcoglycan Complex Recovery
2020 Carotti, Marcello; Scano, Martina; Fancello, Irene; Richard, Isabelle; Risato, Giovanni; Bensalah, Mona; Soardi, Michela; Sandona', Dorianna
Non-genomic mechanisms in the estrogen regulation of glycolytic protein levels in endothelial cells
2020 Boscaro, C.; Carotti, M.; Albiero, M.; Trenti, A.; Fadini, G. P.; Trevisi, L.; Sandona, D.; Cignarella, A.; Bolego, C.
Novel zebrafish models for sarcoglycanopathy
2019 Soardi, Michela; Carotti, Marcello; Bertolucci, Cristiano; Risato, Giovanni; Scano, Martina; Argenton, Francesco; Sacchetto, Roberta; Sandona', Dorianna
Small molecules to rescue folding-defective sarcoglycans: in vivo assessment of novel therapeutic strategies
2019 Sandona', Dorianna; Scano, Martina; Fecchio, Chiara; Bondi', Michela; Carotti, Marcello; Risato, Giovanni; Soardi, Michela; Sacchetto, Roberta
Novel animal models for sarcoglycanopathy
2019 Scano, Martina; Risato, Giovanni; Soardi, Michela; Carotti, Marcello; Sandona', Dorianna
Sarcoglycanopathies, therapeutic approaches based on small molecules
2018 Sandona', Dorianna; Fecchio, Chiara; Carotti, Marcello; Soardi, Michela; Bianchini, Elisa; Sacchetto, Roberta
Repairing folding-defective α-sarcoglycan mutants by CFTR correctors, a potential therapy for Limb Girdle Muscular Dystrophy 2D
2018 Carotti, Marcello; Marsolier, Justine; Soardi, Michela; Bianchini, Elisa; Gomiero, Chiara; Fecchio, Chiara; Henriques, Sara F; Betto, Romeo; Sacchetto, Roberta; Richard, Isabelle; Sandonà, Dorianna
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