Sfoglia per Autore
SEPN1-related myopathy depends on the oxidoreductase ERO1A and is druggable with the chemical chaperone TUDCA
2024 Germani, Serena; Van Ho, Andrew Tri; Cherubini, Alessandro; Varone, Ersilia; Chernorudskiy, Alexander; Renna, Giorgia Maria; Fumagalli, Stefano; Gobbi, Marco; Lucchetti, Jacopo; Bolis, Marco; Guarrera, Luca; Craparotta, Ilaria; Rastelli, Giorgia; Piccoli, Giorgia; de Napoli, Cosimo; Nogara, Leonardo; Poggio, Elena; Brini, Marisa; Cattaneo, Angela; Bachi, Angela; Simmen, Thomas; Cali, Tito; Quijano-Roy, Susana; Boncompagni, Simona; Blaauw, Bert; Ferreiro, Ana; Zito, Ester
A combination of metformin and galantamine exhibits synergistic benefits in the treatment of sarcopenia
2023 Tezze, Caterina; Amendolagine, Francesco Ivan; Nogara, Leonardo; Baraldo, Martina; Ciciliot, Stefano; Arcidiacono, Diletta; Zaramella, Alice; Masiero, Giulio; Ferrarese, Giulia; Realdon, Stefano; Blaauw, Bert; Detienne, Giel; Beliën, Ann Tj; Sandri, Marco; Mercken, Evi M
Defective excitation-contraction coupling and mitochondrial respiration precede mitochondrial Ca2+ accumulation in spinobulbar muscular atrophy skeletal muscle
2023 Marchioretti, Caterina; Zanetti, Giulia; Pirazzini, Marco; Gherardi, Gaia; Nogara, Leonardo; Andreotti, Roberta; Martini, Paolo; Marcucci, Lorenzo; Canato, Marta; R Nath, Samir; Zuccaro, Emanuela; Chivet, Mathilde; Mammucari, Cristina; Pacifici, Marco; Raffaello, Anna; Rizzuto, Rosario; Mattarei, Andrea; Desbats, MARIA ANDREA; Salviati, Leonardo; Megighian, Aram; Sorarù, Gianni; Pegoraro, Elena; Belluzzi, Elisa; Pozzuoli, Assunta; Biz, Carlo; Ruggieri, Pietro; Romualdi, Chiara; P Lieberman, Andrew; J Babu, Gopal; Sandri, Marco; Blaauw, Bert; Basso, Manuela; Pennuto, Maria
Inducible deletion of raptor and mTOR from adult skeletal muscle impairs muscle contractility and relaxation
2022 Baraldo, Martina; Zorzato, Sabrina; Dondjang, Achille Homère Tchampda; Geremia, Alessia; Nogara, Leonardo; Dumitras, Ana Georgia; Canato, Marta; Marcucci, Lorenzo; Nolte, Hendrik; Blaauw, Bert
CFTR corrector C17 is effective in muscular dystrophy, in vivo proof of concept in LGMDR3
2022 Scano, Martina; Benetollo, Alberto; Nogara, Leonardo; Bondì, Michela; DALLA BARBA, Francesco; Soardi, Michela; Furlan, Sandra; Akyurek, EYLEM EMEK; Caccin, Paola; Carotti, Marcello; Sacchetto, Roberta; Blaauw, Bert; Sandonà, Dorianna
Activation of Akt-mTORC1 signalling reverts cancer-dependent muscle wasting
2022 Geremia, Alessia; Sartori, Roberta; Baraldo, Martina; Nogara, Leonardo; Balmaceda, Valeria; Dumitras, Georgia Ana; Ciciliot, Stefano; Scalabrin, Marco; Nolte, Hendrik; Blaauw, Bert
PERM1 interacts with the MICOS-MIB complex to connect the mitochondria and sarcolemma via ankyrin B
2021 Bock, T.; Turk, C.; Aravamudhan, S.; Keufgens, L.; Bloch, W.; Rozsivalova, D. H.; Romanello, V.; Nogara, L.; Blaauw, B.; Trifunovic, A.; Braun, T.; Kruger, M.
Neuromuscular junction instability and altered intracellular calcium handling as early determinants of force loss during unloading in humans
2021 Monti, Elena; Reggiani, Carlo; Franchi, Martino V.; Toniolo, Luana; Sandri, Marco; Armani, Andrea; Zampieri, Sandra; Giacomello, Emiliana; Sarto, Fabio; Sirago, Giuseppe; Murgia, Marta; Nogara, Leonardo; Marcucci, Lorenzo; Ciciliot, Stefano; Šimunic, Boštjan; Pišot, Rado; Narici, Marco V.
In vivo proof of concept of the efficacy of the CFTR corrector C17 in a sarcoglycanopathy mouse model
2021 Scano, Martina; Benetollo, Alberto; Nogara, Leonardo; Bondi', Michela; DALLA BARBA, Francesco; Caccin, Paola; Carotti, Marcello; Sacchetto, Roberta; Blaauw, Bert; Sandona', Dorianna
Protein profile of fiber types in human skeletal muscle: a single-fiber proteomics study
2021 Murgia, Marta; Nogara, Leonardo; Baraldo, Martina; Reggiani, Carlo; Mann, Matthias; Schiaffino, Stefano
Muscle functional recovery is driven by extracellular vesicles combined with muscle extracellular matrix in a volumetric muscle loss murine model
2021 Magarotto, F.; Sgro, A.; Dorigo Hochuli, A. H.; Andreetta, M.; Grassi, M.; Saggioro, M.; Nogara, L.; Tolomeo, A. M.; Francescato, R.; Collino, F.; Germano, G.; Caicci, F.; Maghin, E.; Piccoli, M.; Jurga, M.; Blaauw, B.; Gamba, P.; Muraca, M.; Pozzobon, M.
Raptor is critical for increasing the mitochondrial proteome and skeletal muscle force during hypertrophy
2021 Baraldo, M.; Nogara, L.; Dumitras, G. A.; Tchampda Dondjang, A. H.; Geremia, A.; Scalabrin, M.; Turk, C.; Telkamp, F.; Zentilin, L.; Giacca, M.; Kruger, M.; Blaauw, B.
Exercise-dependent increases in protein synthesis are accompanied by chromatin modifications and increased MRTF-SRF signaling
2020 Solagna, Francesca; Nogara, Leonardo; Dyar, Kenneth A; Greulich, Franziska; Mir, Ashfaq Ali; Türk, Clara; Bock, Theresa; Geremia, Alessia; Baraldo, Martina; Sartori, Roberta; Farup, Jean; Uhlenhaut, Henriette; Vissing, Kristian; Kruger, Marcus; Blaauw, Bert
High-throughput proteomics fiber typing (ProFiT) for comprehensive characterization of single skeletal muscle fibers
2020 Kallabis, S.; Abraham, L.; Muller, S.; Dzialas, V.; Turk, C.; Wiederstein, J. L.; Bock, T.; Nolte, H.; Nogara, L.; Blaauw, B.; Braun, T.; Kruger, M.
KBTBD13 is an actin-binding protein that modulates muscle kinetics
2020 de Winter, Josine M; Molenaar, Joery P; Yuen, Michaela; van der Pijl, Robbert; Shen, Shengyi; Conijn, Stefan; van de Locht, Martijn; Willigenburg, Menne; Bogaards, Sylvia Jp; van Kleef, Esmee Sb; Lassche, Saskia; Persson, Malin; Rassier, Dilson E; Sztal, Tamar E; Ruparelia, Avnika A; Oorschot, Viola; Ramm, Georg; Hall, Thomas E; Xiong, Zherui; Johnson, Christopher N; Li, Frank; Kiss, Balazs; Lozano-Vidal, Noelia; Boon, Reinier A; Marabita, Manuela; Nogara, Leonardo; Blaauw, Bert; Rodenburg, Richard J; Kϋsters, Benno; Doorduin, Jonne; Beggs, Alan H; Granzier, Henk; Campbell, Ken; Ma, Weikang; Irving, Thomas; Malfatti, Edoardo; Romero, Norma B; Bryson-Richardson, Robert J; van Engelen, Baziel Gm; Voermans, Nicol C; Ottenheijm, COEN ADRI CHARLES
Changes in the fraction of strongly attached cross bridges in mouse atrophic and hypertrophic muscles as revealed by continuous wave electron paramagnetic resonance
2019 Galazzo, L.; Nogara, L.; Loverso, F.; Polimeno, A.; Blaauw, B.; Sandri, M.; Reggiani, C.; Carbonera, D.
A maladaptive ER stress response triggers dysfunction in highly active muscles of mice with SELENON loss
2019 Pozzer, D; Varone, E; Chernorudskiy, A; Schiarea, S; Missiroli, S; Giorgi, C; Pinton, P; Canato, M; Germinario, E; Nogara, L; Blaauw, B; Zito, E
Loss of mitochondrial calcium uniporter rewires skeletal muscle metabolism and substrate preference
2019 Gherardi, Gaia; Nogara, Leonardo; Ciciliot, Stefano; Fadini, Gian Paolo; Blaauw, Bert; Braghetta, Paola; Bonaldo, Paolo; De Stefani, Diego; Rizzuto, Rosario; Mammucari, Cristina
Skeletal muscle mTORC1 regulates neuromuscular junction stability
2019 Baraldo, Martina; Geremia, Alessia; Pirazzini, Marco; Nogara, Leonardo; Solagna, Francesca; Türk, Clara; Nolte, Hendrik; Romanello, Vanina; Megighian, Aram; Boncompagni, Simona; Kruger, Marcus; Sandri, Marco; Blaauw, Bert
SELENON (SEPN1) protects skeletal muscle from saturated fatty acid-induced ER stress and insulin resistance
2019 Varone, E; Pozzer, D; Di Modica, S; Chernorudskiy, A; Nogara, L; Baraldo, M; Cinquanta, M; Fumagalli, MADDALENA SONA ABLA; Villar-Quiles, Rn; De Simoni, Mg; Blaauw, B; Ferreiro, A; Zito, E
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