Sfoglia per Autore
Reduced mitochondrial Ca2+ transients stimulate autophagy in human fibroblasts carrying the 13514A>G mutation of the ND5 subunit of NADH dehydrogenase
In corso di stampa Granatiero, Veronica; Giorgio, Valentina; Cali', Tito; Patron, Maria; Brini, Marisa; Bernardi, Paolo; Valeria, Tiranti; Zeviani, Massimo; Giorgia, Pallafacchina; DE STEFANI, Diego; Rizzuto, Rosario
Xenotopic expression of alternative oxidase (AOX) to study mechanisms of mitochondrial disease
2023 Viscomi, Carlo; Moore, Anthony L; Zeviani, Massimo; Szibor, Marten
Drosophila Mpv17 forms an ion channel and regulates energy metabolism
2023 Corrà, Samantha; Checchetto, Vanessa; Brischigliaro, Michele; Rampazzo, Chiara; Bottani, Emanuela; Gagliani, Cristina; Cortese, Katia; De Pittà, Cristiano; Roverso, Marco; De Stefani, Diego; Bogialli, Sara; Zeviani, Massimo; Viscomi, Carlo; Szabò, Ildiko; Costa, Rodolfo
PPAR-gamma agonist pioglitazone recovers mitochondrial quality control in fibroblasts from PITRM1-deficient patients
2023 Di Donfrancesco, Alessia; Berlingieri, Christian; Giacomello, Marta; Frascarelli, Chiara; Magalhaes Rebelo, Ana Paula; Bindoff, Laurence A; Reeval, Segel; Renbaum, Paul; Santorelli, Filippo M; Massaro, Giulia; Viscomi, Carlo; Zeviani, Massimo; Ghezzi, Daniele; Bottani, Emanuela; Brunetti, Dario
Double administration of self-complementary AAV9(NDUFS4) prevents Leigh disease in Ndufs4(-/-) mice
2022 Corra, S; Cerutti, R; Balmaceda, V; Viscomi, C; Zeviani, M
Two respiratory chain organizations with distinct bioenergetic properties coexist in human mitochondria
2022 Fernández-Vizarra, Erika; López-Calcerrada, Sandra; Tzoulis, Charalampos; Pitceathly, Robert D. S.; Zeviani, Massimo; Ugalde, Cristina
CG7630 is the Drosophila melanogaster homolog of the cytochrome c oxidase subunit COX7B
2022 Brischigliaro, Michele; Cabrera-Orefice, Alfredo; Sturlese, Mattia; Elurbe, Dei M; Frigo, Elena; Fernandez-Vizarra, Erika; Moro, Stefano; Huynen, Martijn A; Arnold, Susanne; Viscomi, Carlo; Zeviani, Massimo
Mitochondrial Neurodegeneration
2022 Zeviani, Massimo; Viscomi, Carlo
Mitochondrial Cytochrome c Oxidase Defects Alter Cellular Homeostasis of Transition Metals
2022 Brischigliaro, Michele; Badocco, Denis; Costa, Rodolfo; Viscomi, Carlo; Zeviani, Massimo; Pastore, Paolo; Fernández-Vizarra, Erika
Two independent respiratory chains adapt OXPHOS performance to glycolytic switch
2022 Fernández-Vizarra, Erika; López-Calcerrada, Sandra; Sierra Magro, Ana; Pérez-Pérez, Rafael; Formosa Luke, E; Illescas, María; Peñas, Ana; Brischigliaro, Michele; Ding, Shujing; Fearnley Ian, M; Tzoulis, Charalampos; Pitceathly Robert, Ds; Martín Miguel, Angel; Stroud David, A; Zeviani, Massimo; Ryan Michael, T; Ugalde, Cristina
The relevance of migraine in the clinical spectrum of mitochondrial disorders
2022 Terrin, A.; Bello, L.; Valentino, M. L.; Caporali, L.; Soraru, G.; Carelli, V.; Maggioni, F.; Zeviani, M.; Pegoraro, E.
Mitochondrial disorders of the OXPHOS system
2021 Fernandez-Vizarra, Erika; Zeviani, Massimo
SILAC-based complexome profiling dissects the structural organization of the human respiratory supercomplexes in SCAFIKO cells
2021 Fernández-Vizarra, Erika; López-Calcerrada, Sandra; Formosa, Luke E; Pérez-Pérez, Rafael; Ding, Shujing; Fearnley, Ian M; Arenas, Joaquín; Martín, Miguel A; Zeviani, Massimo; Ryan, Michael T; Ugalde, Cristina
Modelling of BCS1L-related human mitochondrial disease in Drosophila melanogaster
2021 Brischigliaro, M.; Frigo, E.; Corra, S.; De Pitta, C.; Szabo, I.; Zeviani, M.; Costa, R.
Duplexing complexome profiling with SILAC to study human respiratory chain assembly defects
2021 Páleníková, Petra; Harbour, Michael E; Prodi, Federica; Minczuk, Michal; Zeviani, Massimo; Ghelli, Anna; Fernández-Vizarra, Erika
Role of pitrm1 in mitochondrial dysfunction and neurodegeneration
2021 Brunetti, D.; Catania, A.; Viscomi, C.; Deleidi, M.; Bindoff, L. A.; Ghezzi, D.; Zeviani, M.
DNA polymerase gamma mutations that impair holoenzyme stability cause catalytic subunit depletion
2021 Silva-Pinheiro, Pedro; Pardo-Hernández, Carlos; Reyes, Aurelio; Tilokani, Lisa; Mishra, Anup; Cerutti, Raffaele; Li, Shuaifeng; Rozsivalova, Dieu-Hien; Valenzuela, Sebastian; Dogan, Sukru A; Peter, Bradley; Fernández-Silva, Patricio; Trifunovic, Aleksandra; Prudent, Julien; Minczuk, Michal; Bindoff, Laurence; Macao, Bertil; Zeviani, Massimo; Falkenberg, Maria; Viscomi, Carlo
Blue-Native Electrophoresis to Study the OXPHOS Complexes
2021 Fernandez-Vizarra, Erika; Zeviani, Massimo
Exploiting pyocyanin to treat mitochondrial disease due to respiratory complex III dysfunction
2021 Peruzzo, Roberta; Corrà, Samantha; Costa, Roberto; Brischigliaro, Michele; Varanita, Tatiana; Biasutto, Lucia; Rampazzo, Chiara; Ghezzi, Daniele; Leanza, Luigi; Zoratti, Mario; Zeviani, Massimo; De Pittà, Cristiano; Viscomi, Carlo; Costa, Rodolfo; Szabò, Ildikò
NDUFS3 depletion permits complex I maturation and reveals TMEM126A/OPA7 as an assembly factor binding the ND4-module intermediate
2021 D'Angelo, Luigi; Astro, Elisa; De Luise, Monica; Kurelac, Ivana; Umesh-Ganesh, Nikkitha; Ding, Shujing; Fearnley, Ian M; Gasparre, Giuseppe; Zeviani, Massimo; Porcelli, Anna Maria; Fernandez-Vizarra, Erika; Iommarini, Luisa
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