Distribuzione geografica
Continente #
NA - Nord America 6023
EU - Europa 489
AS - Asia 359
SA - Sud America 4
Continente sconosciuto - Info sul continente non disponibili 3
OC - Oceania 1
Totale 6879
Nazione #
US - Stati Uniti d'America 6020
CN - Cina 302
IT - Italia 108
FI - Finlandia 104
SE - Svezia 88
DE - Germania 81
UA - Ucraina 49
GB - Regno Unito 33
VN - Vietnam 29
IN - India 18
IE - Irlanda 8
FR - Francia 6
HK - Hong Kong 6
BR - Brasile 4
CA - Canada 3
EU - Europa 3
RU - Federazione Russa 3
AZ - Azerbaigian 2
BE - Belgio 2
ES - Italia 2
NL - Olanda 2
AT - Austria 1
CH - Svizzera 1
JP - Giappone 1
NZ - Nuova Zelanda 1
PH - Filippine 1
PL - Polonia 1
Totale 6879
Città #
Fairfield 1066
Woodbridge 841
Houston 561
Chandler 556
Ann Arbor 498
Cambridge 411
Ashburn 400
Seattle 361
Wilmington 350
Jacksonville 225
Princeton 128
San Diego 108
Beijing 105
Des Moines 82
Padova 61
Nanjing 57
Roxbury 55
Medford 54
Helsinki 38
Boardman 36
Dong Ket 28
Shenyang 22
Jinan 19
Nanchang 19
Hebei 16
Changsha 12
London 11
Falls Church 10
Jiaxing 9
Tianjin 8
Norwalk 7
Zhengzhou 6
Aprilia 4
Dublin 4
Lipomo 4
Ningbo 4
Redwood City 4
Detroit 3
Fuzhou 3
Indiana 3
Rome 3
Baku 2
Belo Horizonte 2
Borås 2
Brendola 2
Brussels 2
Camparada 2
Ferrara 2
Galway 2
Haikou 2
Hangzhou 2
Hanover 2
Kharkiv 2
Kunming 2
Misterbianco 2
Mountain View 2
New York 2
Nürnberg 2
Taiyuan 2
Taizhou 2
Toronto 2
Yellow Springs 2
A Coruña 1
Afragola 1
Alghero 1
Assisi 1
Auburn Hills 1
Bologna 1
Casier 1
Casièr 1
Chiampo 1
Conegliano 1
Copperas Cove 1
Costa Mesa 1
Davao City 1
Florence 1
Geislingen an der Steige 1
Groningen 1
Guangzhou 1
Guidonia 1
Halberstadt 1
Hefei 1
Hollywood 1
Huzhou 1
Jesi 1
Lanzhou 1
Leawood 1
Lozzo Atestino 1
Martellago 1
Milan 1
Monselice 1
Montoro 1
Munich 1
Nanning 1
Napoli 1
Nha Trang 1
Orange 1
Phoenix 1
Pinehaven 1
Raleigh 1
Totale 6272
Nome #
F-actin dynamics regulates mammalian organ growth and cell fate maintenance 196
Loss of mitochondrial calcium uniporter rewires skeletal muscle metabolism and substrate preference 148
The ablation of the matricellular protein EMILIN2 causes defective vascularization due to impaired EGFR-dependent IL-8 production affecting tumor growth 143
The cyclophilin inhibitor Debio 025 normalizes mitochondrial function, muscle apoptosis and ultrastructural defects in Col6a1-/- myopathic mice 138
An enhancer required for transcription of the Col6a1 gene in muscle connective tissue is induced by signals released from muscle cells. 119
Distinct regions control transcriptional activation of the alpha1(VI) collagen promoter in different tissues of transgenic mice. 116
Overlapping, complementary and site-specific expression pattern of genes of the EMILIN/Multimerin family 112
Cyclosporin A Promotes in vivo Myogenic Response in Collagen VI-Deficient Myopathic Mice. 110
Collagen VI deficiency induces early onset myopathy in the mouse: an animal model for Bethlem myopathy 107
Wnt/b-catenin pathway in arrhythmogenic cardiomyopathy 106
Mitochondrial dysfunction and apoptosis in myopathic mice with collagen VI deficiency 106
O.14 Biocompatible nanoparticles as slow-release delivery system of 2′OMePS AON administered both intraperitoneally and orally in the mdx mice: dystrophin rescue and nanoparticles biodistribution 101
EMILIN3, an extracellular matrix molecule with restricted distribution in skin 100
AMBRA1 Controls Regulatory T-Cell Differentiation and Homeostasis Upstream of the FOXO3-FOXP3 Axis 100
Mechanisms of transcriptional activation of the Col6a1 gene during Schwann cell differentiation 99
Emilin genes are duplicated and dynamically expressed during zebrafish embryonic development 98
First steps to define murine amniotic fluid stem cell microenvironment 98
Loss of EMILIN-1 Enhances Arteriolar Myogenic Tone Through TGF-β (Transforming Growth Factor-β)-Dependent Transactivation of EGFR (Epidermal Growth Factor Receptor) and Is Relevant for Hypertension in Mice and Humans 98
Hmga2 promoter analysis in transgenic mice 96
An ultrastructural approach to the adaptive role of the cell wall in the intertidal algaFucus virsoides 96
Cell type-specific transcription of the alpha 1(VI) collagen gene - Role of the AP1 binding site and of the core promoter 95
Dystrophin restoration in skeletal, heart and skin arrector pili smooth muscle of mdx mice by ZM2 NP-AON complexes. 94
Cyclosporin A promotes in vivo myogenic response in collagen VI-deficient myopathic mice 92
Role of adiponectin in the metabolism of skeletal muscles in collagen VI–related myopathies 92
Collagen VI deficiency affects the organization of fibronectin in the extracellular matrix of cultured fibroblasts 91
Oxidative stress by monoamine oxidases is causally involved in myofiber damage in muscular dystrophy. 91
Muscle proteomics reveals novel insights into the pathophysiological mechanisms of collagen vi myopathies 91
EMILIN-1 deficiency induces elastogenesis and vascular cell defects 90
NIM811, a cyclophilin inhibitor without immunosuppressive activity, is beneficial in collagen VI congenital muscular dystrophy models. 90
Intracellular targetting signals of polymeric immunoglobulin receptors are highly conserved between species 89
Cyclosporin A corrects mitochondrial dysfunction and muscle apoptosis in patients with collagen VI myopathies. 88
Cationic PMMA nanoparticles bind and deliver antisense oligoribonucleotides allowing restoration of dystrophin expression in the mdx mouse. 87
Persistent Dystrophin Protein Restoration 90 Days after a Course of Intraperitoneally Administered Naked 2′OMePS AON and ZM2 NP-AON Complexes in mdx Mice 86
Biodistribution Studies of Polymeric Nanoparticles for Drug Delivery in Mice 83
Lentiviral-mediated RNAi in vivo silencing of Col6a1, a gene with complex tissue specific expression pattern 83
Vascular Smooth Muscle Emilin-1 Is a Regulator of Arteriolar Myogenic Response and Blood Pressure 79
Changes in Muscle Cell Metabolism and Mechanotransduction Are Associated with Myopathic Phenotype in a Mouse Model of Collagen VI Deficiency 79
Deep RNA profiling identified CLOCK and molecular clock genes as pathophysiological signatures in collagen VI myopathy 79
Gelatin-genipin-based biomaterials for skeletal muscle tissue engineering 78
FGF signaling deregulation is associated with early developmental skeletal defects in animal models for mucopolysaccharidosis type II (MPSII). 78
A novel murine model for arrhythmogenic cardiomyopathy points to a pathogenic role of Wnt signaling and miRNA dysregulation. 77
The Polyphenol Pterostilbene Ameliorates the Myopathic Phenotype of Collagen VI Deficient Mice via Autophagy Induction 75
Preclinical PK and PD studies on 2'-O-methyl-phosphorothioate RNA antisense oligonucleotides in the mdx mouse model. 74
T.P.22 Nanoparticles as delivery systems for antisense oligoribonucleotides: Biodistribution studies and definition of the release kinetic in treated mdx mice 73
Extracellular collagen VI has prosurvival and autophagy instructive properties in mouse fibroblasts 72
P1.52 BIO-NMD: Discovery and validation of biomarkers for neuromuscular diseases (NMDs) – An EU funded FP7 project 71
Pathogenic Potential of Hic1-Expressing Cardiac Stromal Progenitors 71
The systemic administration of a low dose of 20MePS-AON combined with novel cationic polymethylmethacrylate nanoparticles induces the rescue of dystrophin expression in the mdx murine model 70
Multimerin-2 maintains vascular stability and permeability 70
Expression of EMILIN-1 gene in mouse development 69
NG2/CSPG4-collagen type VI interplays putatively involved in the microenvironmental control of tumour engraftment and local expansion. 69
EMILIN-3, a peculiar member of the EMILIN/Multimerin protein family, has a distinct expression pattern, forms oligomeric assemblies and serves as a pro TGF-β antagonist. 69
Mapping Wnt/beta-catenin signaling during mouse development and in colorectal tumors. 67
Tissue-specific expression of promoter regions of the alpha1(VI) collagen gene in cell cultures and transgenic mice. 66
Collagen VI null mice as a model for early onset muscle decline in aging 65
Fra-2-expressing macrophages promote lung fibrosis in mice 63
M.P.1.01 Pilot trial with cyclosporin A in patients with collagen VI myopathies 60
Emilin1 links TGF-beta maturation to blood pressure homeostasis 59
Elastic fiber proteins in the glomerular mesangium in vivo and in culture 58
Biodistribution and molecular studies on orally administered nanoparticle-AON complexes encapsulated with alginate aiming at inducing dystrophin rescue in mdx mice. 58
Analysis of beta cell proliferation dynamics in zebrafish 58
Collagen VI in healthy and diseased nervous system 58
Electrospun structures made of a hydrolyzed keratin-based biomaterial for development of in vitro tissue models 56
S12.28 Rescue of myopathic collagen VI null mice by genetic inactivation of mitochondrial cyclophilin d 55
EM.P.5.07 Abnormal elastin deposits and altered organization of elastic fibers in collagen VI- related disorders 54
Analysis of transcription of the Col6a1 gene in a specific set of tissues suggests a new variant of enhancer region 53
Is beta-catenin signalling involved in the molecular pathogenesis of arrhythmogenic right ventricular cardiomyopathy? Study on DSG2 transgenic mice 48
Analysis of regulatory regions of Emilin1 gene and their combinatorial contribution to tissue-specific transcription 46
Ultrastructural and cytochemical study on pit connections of Pterocladia pinnata (Huds.) Papenf. (Gelidiales) 43
Study of the molecular pathogenesis of arrhythmogenic cardiomyopathy due to Desmoglein-2 mutations: the zebrafish helps the mouse 43
Tumor cell NG2 proteoglycan controls cancer progression through its interaction with host Collagen type VI 42
The expression of Emilin-1 in vascular smooth muscle cells regulates arteriolar myogenic response and blood pressure 40
Mmrn2 null mice are hypertensive: dissecting the role of VSMCs and ECs 39
Targeting Interleukin-1β Protects from Aortic Aneurysms Induced by Disrupted Transforming Growth Factor β Signaling 38
EM.P.5.03 The cyclophilin inhibitor Debio 025 normalizes mitochondrial function, muscle apoptosis and ultrastructural defects in Col6a1-/- myopathic mice 35
Ablation of collagen VI leads to the release of platelets with altered function 26
Expression pattern and function analysis of Emilin genes in zebrafish 21
Emilin-2 is a component of bone marrow extracellular matrix regulating mesenchymal stem cell differentiation and hematopoietic progenitors 19
Generation of a floxed allele of extracellular matrix protein Emilin1 to study its role in vascular structure and in the regulation of blood pressure in the mouse 17
Ambra1 deficiency impairs mitophagy in skeletal muscle 12
La questione animale: il caso della sperimentazione tra razionale scientifico e dibattito etico-pubblico 12
Lack of COL6/collagen VI causes megakaryocyte dysfunction by impairing autophagy and inducing apoptosis 9
Collagen VI deficiency causes behavioral abnormalities and cortical dopaminergic dysfunction 7
Corrigendum: FGF signaling deregulation is associated with early developmental skeletal defects in animal models for mucopolysaccharidosis type II (MPSII) [Human Molecular Genetics, 27, 13, (2018) (2262-2275)] DOI: 10.1093/hmg/ddy131 4
Emerging Perspectives on the Rare Tubulopathy Dent Disease: Is Glomerular Damage a Direct Consequence of ClC-5 Dysfunction? 3
EMILIN1 deficiency causes arterial tortuosity with osteopenia and connects impaired elastogenesis with defective collagen fibrillogenesis 1
Totale 6930
Categoria #
all - tutte 12244
article - articoli 11933
book - libri 0
conference - conferenze 0
curatela - curatele 0
other - altro 0
patent - brevetti 0
selected - selezionate 0
volume - volumi 37
Totale 24214

Totale Lug Ago Sett Ott Nov Dic Gen Feb Mar Apr Mag Giu
2017/201863 0000 00 00 82512
2018/2019817 82541 101 1933 3177278231
2019/20201686 2206424143 164127 151198 19820713357
2020/20211138 57695653 80103 74126 16811714194
2021/20221249 44120193112 5456 66143 5619137249
2022/2023982 18812714137 158164 1182 101000
Totale 6930