BONALDO, PAOLO
 Distribuzione geografica
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Continente #
NA - Nord America 13.636
EU - Europa 1.317
AS - Asia 855
SA - Sud America 7
OC - Oceania 5
AF - Africa 2
Continente sconosciuto - Info sul continente non disponibili 2
Totale 15.824
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Nazione #
US - Stati Uniti d'America 13.619
CN - Cina 715
IT - Italia 360
FI - Finlandia 307
DE - Germania 154
SE - Svezia 150
GB - Regno Unito 127
UA - Ucraina 121
IN - India 59
VN - Vietnam 53
FR - Francia 24
IE - Irlanda 19
CA - Canada 16
HK - Hong Kong 15
NL - Olanda 10
RU - Federazione Russa 10
GR - Grecia 7
BR - Brasile 6
ES - Italia 5
AU - Australia 4
BE - Belgio 4
NO - Norvegia 4
CH - Svizzera 3
HR - Croazia 3
TR - Turchia 3
AT - Austria 2
EU - Europa 2
IR - Iran 2
SG - Singapore 2
AR - Argentina 1
BD - Bangladesh 1
BG - Bulgaria 1
CZ - Repubblica Ceca 1
HU - Ungheria 1
IL - Israele 1
JP - Giappone 1
KH - Cambogia 1
KR - Corea 1
LU - Lussemburgo 1
MM - Myanmar 1
MX - Messico 1
NG - Nigeria 1
NZ - Nuova Zelanda 1
PL - Polonia 1
RO - Romania 1
SC - Seychelles 1
SI - Slovenia 1
Totale 15.824
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Città #
Fairfield 2.260
Woodbridge 1.909
Houston 1.309
Ann Arbor 1.168
Chandler 1.054
Ashburn 946
Seattle 780
Cambridge 755
Wilmington 728
Jacksonville 548
Princeton 293
San Diego 234
Beijing 208
Des Moines 150
Helsinki 142
Padova 138
Nanjing 116
Medford 114
Roxbury 108
Boardman 95
Dong Ket 53
Guangzhou 53
New York 53
Hebei 40
Shenyang 33
Nanchang 32
Jinan 28
London 26
Norwalk 24
Changsha 21
Pune 21
Jiaxing 20
Redwood City 19
Shanghai 19
Ogden 18
Milan 16
Dublin 15
Tianjin 15
Falls Church 14
Paris 13
Aprilia 12
Rome 12
Ningbo 11
Zhengzhou 10
Detroit 9
Kilburn 9
Tappahannock 9
Haikou 8
Indiana 8
Hounslow 7
Selvazzano Dentro 7
Washington 7
Hefei 6
Kharkiv 6
Arlington 5
Borås 5
Camparada 5
Ottawa 5
Cadillac 4
Chengdu 4
Chiampo 4
Groningen 4
Lanzhou 4
Lipomo 4
Los Angeles 4
Munich 4
Taizhou 4
Vicenza 4
Brussels 3
Catania 3
Chiswick 3
Ferrara 3
Florence 3
Fuzhou 3
Hangzhou 3
Hanover 3
Kunming 3
Lappeenranta 3
Magenta 3
Montréal 3
Orange 3
Phoenix 3
Portland 3
Prescot 3
Rockville 3
Southwark 3
Stockholm 3
Taiyuan 3
Turin 3
Yellow Springs 3
Abano Terme 2
Acton 2
Belo Horizonte 2
Bologna 2
Brendola 2
Busto Arsizio 2
Galway 2
Giudecca 2
Islington 2
Krasnoyarsk 2
Totale 13.855
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Nome #
Glycolytic-to-oxidative fiber-type switch and mTOR signaling activation are early-onset features of SBMA muscle modified by high-fat diet 184
Zebrafish ambra1a and ambra1b knockdown impairs skeletal muscle development 182
The epg5 knockout zebrafish line: a model to study Vici syndrome 176
Perturbations in cell signaling elicit early cardiac defects in mucopolysaccharidosis type II 174
Loss of mitochondrial calcium uniporter rewires skeletal muscle metabolism and substrate preference 159
Glycolytic-to-oxidative fiber-type switch and mTOR signaling activation are early-onset features of SBMA muscle modified by high-fat diet 157
The ablation of the matricellular protein EMILIN2 causes defective vascularization due to impaired EGFR-dependent IL-8 production affecting tumor growth 154
The cyclophilin inhibitor Debio 025 normalizes mitochondrial function, muscle apoptosis and ultrastructural defects in Col6a1-/- myopathic mice 142
Physical exercise stimulates autophagy in normal skeletal muscles but is detrimental for collagen VI deficient muscles. 142
Identification of a deep intronic mutation in the COL6A2 gene by a novel custom oligonucleotide CGH array designed to explore allelic and genetic heterogeneity in collagen VI-related myopathies. 138
Autophagy is defective in collagen VI muscular dystrophies, and its reactivation rescues myofiber degeneration. 138
Collagen VI Ablation Retards Brain Tumor Progression Due to Deficits in Assembly of the Vascular Basal Lamina 133
Lack of Collagen VI Promotes Wound-Induced Hair Growth 130
Guidelines for the use and interpretation of assays for monitoring autophagy (3rd edition) 130
Transcription Factor EB Controls Metabolic Flexibility during Exercise 129
Autosomal recessive myosclerosis myopathy is a collagen VI disorder 125
An enhancer required for transcription of the Col6a1 gene in muscle connective tissue is induced by signals released from muscle cells. 124
Cyclosporin A Promotes in vivo Myogenic Response in Collagen VI-Deficient Myopathic Mice. 123
Distinct regions control transcriptional activation of the alpha1(VI) collagen promoter in different tissues of transgenic mice. 122
Collagen VI regulates peripheral nerve regeneration by modulating macrophage recruitment and polarization 120
Isolation of cDNA clones corresponding to the Mr=150,000 subunit of chick type VI collagen. 118
Multiple forms of chicken alpha3(VI) collagen chain generated by alternative splicing in type A repeated domains. 117
Collagen VI deficiency induces early onset myopathy in the mouse: an animal model for Bethlem myopathy 115
Autophagy activation in COL6 myopathic patients by a low-protein-diet pilot trial 113
Overlapping, complementary and site-specific expression pattern of genes of the EMILIN/Multimerin family 112
Genetic ablation of cyclophilin D rescues mitochondrial defects and prevents muscle apoptosis in collagen VI myopathic mice. 111
AMBRA1 Controls Regulatory T-Cell Differentiation and Homeostasis Upstream of the FOXO3-FOXP3 Axis 111
Critical evaluation of the use of cell cultures for inclusion in clinical trials of patients affected by collagen VI myopathies 109
Fine-tuning of ULK1 mRNA and protein levels is required for autophagy oscillation 107
Mitochondrial dysfunction and apoptosis in myopathic mice with collagen VI deficiency 107
Altered Threshold of the Mitochondrial Permeability Transition Pore in Ullrich Congenital Muscular Dystrophy 106
Emilin genes are duplicated and dynamically expressed during zebrafish embryonic development 106
Mitochondrial dysfunction in the pathogenesis of Ullrich congenital muscular dystrophy and prospective therapy with cyclosporins 106
First steps to define murine amniotic fluid stem cell microenvironment 106
Monoamine oxidase inhibition prevents mitochondrial dysfunction and apoptosis in myoblasts from patients with collagen VI myopathies 106
O.14 Biocompatible nanoparticles as slow-release delivery system of 2′OMePS AON administered both intraperitoneally and orally in the mdx mice: dystrophin rescue and nanoparticles biodistribution 105
Emilin3 is required for notochord sheath integrity and interacts with Scube2 to regulate notochord-derived Hedgehog signals. 105
EMILIN3, an extracellular matrix molecule with restricted distribution in skin 105
Identification and characterization of novel collagen VI non-canonical splicing mutations causing ullrich congenital muscular dystrophy. 104
Loss of EMILIN-1 Enhances Arteriolar Myogenic Tone Through TGF-β (Transforming Growth Factor-β)-Dependent Transactivation of EGFR (Epidermal Growth Factor Receptor) and Is Relevant for Hypertension in Mice and Humans 104
Autophagy activation in COL6 myopathic patients by a low-protein-diet pilot trial 104
Collagen VI is required for the structural and functional integrity of the neuromuscular junction 103
Multiple binding reactivities of an IgG1 mouse monoclonal antibody raised against the extracellular matrix glycoprotein gp 115. 102
Cyclosporin A promotes in vivo myogenic response in collagen VI-deficient myopathic mice 101
Three novel collagen VI chains with high homology to the α3 chain 101
Mechanisms of transcriptional activation of the Col6a1 gene during Schwann cell differentiation 100
Dystrophin restoration in skeletal, heart and skin arrector pili smooth muscle of mdx mice by ZM2 NP-AON complexes. 99
Collagen VI regulates satellite cell self-renewal and muscle regeneration 99
EMILIN-1 deficiency induces elastogenesis and vascular cell defects 98
Altered Trabecular Bone Structure and Delayed Cartilage Degeneration in the Knees of Collagen VI Null Mice 98
Autophagy-mediated regulation of macrophages and its applications for cancer. 98
Oxidative stress by monoamine oxidases is causally involved in myofiber damage in muscular dystrophy. 98
Cationic PMMA nanoparticles bind and deliver antisense oligoribonucleotides allowing restoration of dystrophin expression in the mdx mouse. 98
Aggresome-autophagy involvement in a sarcopenic patient with rigid spine syndrome and a p.C150R mutation in FHL1 gene 98
Cyclosporin A corrects mitochondrial dysfunction and muscle apoptosis in patients with collagen VI myopathies. 97
Altered expression of the MCSP/NG2 chondroitin sulfate proteoglycan in collagen VI deficiency 95
Collagen VI deficiency affects the organization of fibronectin in the extracellular matrix of cultured fibroblasts 95
Autosomal recessive Bethlem myopathy 95
NIM811, a cyclophilin inhibitor without immunosuppressive activity, is beneficial in collagen VI congenital muscular dystrophy models. 95
Collagen VI in cancer and its biological mechanisms. 94
Collagen VI-NG2 axis in human tendon fibroblasts under conditions mimicking injury response 94
Gene trap expression and mutational analysis for genes involved in the development of the mammalian nervous system. 93
Dysfunctional tendon collagen fibrillogenesis in collagen VI null mice. 93
Evidence for the stochastic integration of gene trap vectors into the mouse germline. 93
Muscle proteomics reveals novel insights into the pathophysiological mechanisms of collagen vi myopathies 93
A novel murine model for arrhythmogenic cardiomyopathy points to a pathogenic role of Wnt signaling and miRNA dysregulation. 93
Persistent Dystrophin Protein Restoration 90 Days after a Course of Intraperitoneally Administered Naked 2′OMePS AON and ZM2 NP-AON Complexes in mdx Mice 92
Collagen VI regulates peripheral nerve myelination and function. 92
Lentiviral-mediated RNAi in vivo silencing of Col6a1, a gene with complex tissue specific expression pattern 92
Stable expression of chicken type VI collagen alpha1, alpha2, and alpha3 cDNAs in murine NIH/3T3 cells. 91
The human type VI collagen gene: mRNA and protein variants of the alpha3 chain generated by alternative splicing of an additional 5'-end exon. 91
Characterization of a rare case of Ullrich congenital muscular dystrophy due to truncating mutations within the COL6A1 gene C-terminal domain: a case report. 91
Biosynthesis of chick type VI collagen. I: Intracellular assembly and molecular structure. 90
Critical evaluation of the use of cell cultures for inclusion in clinical trials of patients affected by collagen VI myopathies 90
Gelatin-genipin-based biomaterials for skeletal muscle tissue engineering 90
Structure, chromosomal localization, and promoter analysis of the human Elastin Microfibril Interfase Located proteIN (EMILIN) gene 89
Absence of Type VI Collagen Paradoxically Improves Cardiac Function, Structure, and Remodeling After Myocardial Infarction 89
Guidelines for the use and interpretation of assays for monitoring autophagy (4th edition)1 88
The Role of Collagens in Peripheral Nerve Myelination and Function 88
Structural and Functional Features of the α3 Chain Indicate a Bridging Role for Chicken Collagen VI in Connective Tissues 88
Differential and restricted expression of novel collagen VI chains in mouse. 87
Adipocyte-derived collagen VI affects early mammary tumor progression in vivo, demonstrating a critical interaction in the tumor/stroma microenvironment. 86
Lack of collagen VI promotes neurodegeneration by impairing autophagy and inducing apoptosis during aging 85
Autophagy in Skeletal Muscle Homeostasis and in Muscular Dystrophies 84
The Polyphenol Pterostilbene Ameliorates the Myopathic Phenotype of Collagen VI Deficient Mice via Autophagy Induction 84
Changes in Muscle Cell Metabolism and Mechanotransduction Are Associated with Myopathic Phenotype in a Mouse Model of Collagen VI Deficiency 83
The superfamily of proteins with von Willebrand Factor type A-like domains: one theme common to components of extracellular matrix, hemostasis, cellular adhesion, and defense mechanisms. 83
Antisense-Induced Messenger Depletion Corrects a COL6A2 Dominant Mutation in Ullrich Myopathy. 83
Expression of collagen VI α5 and α6 chains in human muscle and in Duchenne muscular dystrophy-related muscle fibrosis 82
Extracellular matrix: A dynamic microenvironment for stem cell niche. 82
Deep RNA profiling identified CLOCK and molecular clock genes as pathophysiological signatures in collagen VI myopathy 82
Expression of EMILIN-1 gene in mouse development 81
Mitochondrial dysfunction and defective autophagy in the pathogenesis of collagen VI muscular dystrophies. 81
Cyclosporine A in Ullrich congenital muscular dystrophy: long-term results. 80
Extracellular collagen VI has prosurvival and autophagy instructive properties in mouse fibroblasts 80
Biosynthesis of chick type VI collagen. II: Processing and secretion in fibroblasts and smooth muscle cells. 79
Targeting of EMILIN-1 and EMILIN-2 to Fibrillin Microfibrils Facilitates their Incorporation into the Extracellular Matrix 79
Monoclonal antibodies for the different chains of chick type VI collagen. 78
EMILIN2 down-modulates the Wnt signalling pathway and suppresses breast cancer cell growth and migration. 78
Cardiac glycoside ouabain induces autophagic cell death in non-small cell lung cancer cells via a JNK-dependent decrease of Bcl-2 78
Totale 10.478
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Categoria #
all - tutte 53.614
article - articoli 52.010
book - libri 0
conference - conferenze 0
curatela - curatele 0
other - altro 0
patent - brevetti 382
selected - selezionate 0
volume - volumi 940
Totale 106.946
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Totale Lug Ago Sett Ott Nov Dic Gen Feb Mar Apr Mag Giu
2018/20191.354 0 0 0 0 0 0 0 0 0 333 567 454
2019/20203.504 432 127 78 294 375 279 330 436 392 386 254 121
2020/20212.377 108 157 121 228 141 157 144 242 341 246 300 192
2021/20222.708 102 306 399 211 111 110 143 336 93 49 314 534
2022/20232.093 407 242 50 248 357 266 4 130 230 24 102 33
2023/2024943 76 167 152 93 93 144 87 56 43 32 0 0
Totale 15.984