Auditory function in patients with charcot-marie-tooth syndrome

The Charcot-Marie-Tooth (CMT) disease is a neurological syndrome, which has seldom been associated with hearing dysfunction, particularly sudden sensorineural hearing loss (SNHL). The disease of Charcot-Marie-Tooth is due to the alteration of one or more geniuses that give way to the formation of the assone and the genesis of the myelin, whose synthetic deficit involves the reduction of the speed of nervous management . The aim of the study was to detect in individuals suffering from Charcot-Marie-Tooth syndrome with audiological signs and symptoms qualitative and quantitative type of hearing impairment and of these finds some assumptions on the location of the damage along the auditory nerve pathways.