Sfoglia per Autore
Cyclosporin A promotes in vivo myogenic response in collagen VI-deficient myopathic mice
2014 Gattazzo, Francesca; Molon, Sibilla; Morbidoni, Valeria; Braghetta, Paola; Blaauw, Bert; Urciuolo, Anna; Bonaldo, Paolo
The expression of Emilin-1 in vascular smooth muscle cells regulates arteriolar myogenic response and blood pressure
2013 Braghetta, Paola; Bizzotto, Dario; Carnevale, D; DA ROS, Francesco; Litteri, G; D'Urso, A; Cifelli, G; Landolfi, A; Facchinello, Nicola; Colombatti, A; Volpin, Dino; Lembo, G; Bressan, Giorgio
Changes in Muscle Cell Metabolism and Mechanotransduction Are Associated with Myopathic Phenotype in a Mouse Model of Collagen VI Deficiency
2013 Sara De, Palma; Roberta, Leone; Grumati, Paolo; Michele, Vasso; Roman, Polishchuk; Daniele, Capitanio; Braghetta, Paola; Bernardi, Paolo; Bonaldo, Paolo; Cecilia, Gelfi
NG2/CSPG4-collagen type VI interplays putatively involved in the microenvironmental control of tumour engraftment and local expansion.
2013 Cattaruzza, S; Nicolosi, Pa; Braghetta, Paola; Pazzaglia, L; Benassi, Ms; Picci, P; Lacrima, K; Zanocco, D; Rizzo, Erika; Stallcup, Wb; Colombatti, A; Perris, R.
Biodistribution and molecular studies on orally administered nanoparticle-AON complexes encapsulated with alginate aiming at inducing dystrophin rescue in mdx mice.
2013 Falzarano, Ms; Passarelli, C; Bassi, E; Fabris, M; Perrone, D; Sabatelli, P; Maraldi, Nm; Donà, S; Selvatici, R; Bonaldo, Paolo; Sparnacci, K; Laus, M; Braghetta, Paola; Rimessi, P; Ferlini, A.
Persistent Dystrophin Protein Restoration 90 Days after a Course of Intraperitoneally Administered Naked 2′OMePS AON and ZM2 NP-AON Complexes in mdx Mice
2012 Elena, Bassi; Sofia, Falzarano; Marina, Fabris; Francesca, Gualandi; Luciano, Merlini; Gaetano, Vattemi; Daniela, Perrone; Elena, Marchesi; Patrizia, Sabatelli; Katia, Sparnacci; Michele, Laus; Bonaldo, Paolo; Paola, Rimessi; Braghetta, Paola; Alessandra, Ferlini
Study of the molecular pathogenesis of arrhythmogenic cardiomyopathy due to Desmoglein-2 mutations: the zebrafish helps the mouse
2012 Beffagna, Giorgia; Lorenzon, Alessandra; Milanetto, Martina; Doliana, R; Lembo, G; Sabatelli, P; Carnevale, D; Grumati, Paolo; Dazzo, Emanuela; Moro, Enrico; Argenton, Francesco; Bonaldo, Paolo; Braghetta, Paola; Rampazzo, Alessandra
T.P.22 Nanoparticles as delivery systems for antisense oligoribonucleotides: Biodistribution studies and definition of the release kinetic in treated mdx mice
2012 M. S., Falzarano; C., Passarelli; J., van Deutekom; E., Bassi; M., Fabris; P., Sabatelli; K., Sparnacci; M., Laus; Bonaldo, Paolo; Braghetta, Paola; A., Ferlini
Vascular Smooth Muscle Emilin-1 Is a Regulator of Arteriolar Myogenic Response and Blood Pressure
2012 Litteri, Gaia; D., Carnevale; A., D'Urso; G., Cifelli; Braghetta, Paola; A., Damato; Bizzotto, Dario; A., Landolfi; DA ROS, Francesco; P., Sabatelli; Facchinello, Nicola; A., Maffei; Volpin, Dino; A., Colombatti; Bressan, Giorgio; G., Lembo
EMILIN-3, a peculiar member of the EMILIN/Multimerin protein family, has a distinct expression pattern, forms oligomeric assemblies and serves as a pro TGF-β antagonist.
2012 Schiavinato, A; Becker, Ak; Zanetti, Miriam; Corallo, Diana; Milanetto, M; Bizzotto, D; Bressan, Giorgio; Guljelmovic, M; Paulsson, M; Wagener, R; Braghetta, Paola; Bonaldo, Paolo
Mmrn2 null mice are hypertensive: dissecting the role of VSMCs and ECs
2011 Braghetta, Paola; Facchinello, ; Da, Ros; Carnevale, Volpin; Lembo, Bressan
O.14 Biocompatible nanoparticles as slow-release delivery system of 2′OMePS AON administered both intraperitoneally and orally in the mdx mice: dystrophin rescue and nanoparticles biodistribution
2011 A., Ferlini; P., Rimessi; E., Bassi; M. S., Falzarano; M., Fabris; D., Perrone; P., Sabatelli; N. M., Maraldi; K., Sparnacci; M., Laus; Bonaldo, Paolo; Braghetta, Paola
P1.52 BIO-NMD: Discovery and validation of biomarkers for neuromuscular diseases (NMDs) – An EU funded FP7 project
2011 V., Straub; A., Aartsma Rus; C., Al Khalili Szigyarto; C., Béroud; Bonaldo, Paolo; P., Borgiani; Braghetta, Paola; A., Chaouch; S., Cirak; L., Courtot; N., Daraselia; C., Gelfi; P. A. C., ’t Hoen; E., Kotelnikova; Y., Le Priol; H., Lochmueller; J., Morgan; F., Muntoni; G., Novelli; N., Paolillo; R., Tanzi; C., Turner; M., Uhlen; A., Ferlini
Is beta-catenin signalling involved in the molecular pathogenesis of arrhythmogenic right ventricular cardiomyopathy? Study on DSG2 transgenic mice
2010 Beffagna, Giorgia; Lorenzon, Alessandra; Sabatelli, P; Doliana, R; Grumati, Paolo; Carnevale, D; Lembo, G; Bonaldo, Paolo; Braghetta, Paola; Rampazzo, Alessandra
Generation of a floxed allele of extracellular matrix protein Emilin1 to study its role in vascular structure and in the regulation of blood pressure in the mouse
2010 Facchinello, Litteri; Vecchione, Bizzotto; Lembo, Cifelli; Volpin, Bressan; Braghetta, Paola
Oxidative stress by monoamine oxidases is causally involved in myofiber damage in muscular dystrophy.
2010 Menazza, Sara; Blaauw, Bert; Tiepolo, Tania; Toniolo, Luana; Braghetta, Paola; Spolaore, Barbara; Reggiani, Carlo; DI LISA, Fabio; Bonaldo, Paolo; Canton, Marcella
Dystrophin restoration in skeletal, heart and skin arrector pili smooth muscle of mdx mice by ZM2 NP-AON complexes.
2010 Ferlini, A; Sabatelli, P; Fabris, M; Bassi, E; Falzarano, S; Vattemi, G; Perrone, D; Gualandi, F; Maraldi, Nm; Merlini, L; Sparnacci, K; Laus, M; Caputo, Antonella; Bonaldo, Paolo; Braghetta, Paola; Rimessi, P.
Preclinical PK and PD studies on 2'-O-methyl-phosphorothioate RNA antisense oligonucleotides in the mdx mouse model.
2010 Heemskerk, H; de Winter, C; van Kuik, P; Heuvelmans, N; Sabatelli, P; Rimessi, P; Braghetta, Paola; van Ommen, Gj; de Kimpe, S; Ferlini, A; Aartsma Rus, A; van Deutekom, Jc
Cationic PMMA nanoparticles bind and deliver antisense oligoribonucleotides allowing restoration of dystrophin expression in the mdx mouse.
2009 Rimessi, P; Sabatelli, P; Fabris, M; Braghetta, Paola; Bassi, E; Spitali, P; Vattemi, G; Tomelleri, G; Mari, L; Perrone, D; Medici, A; Neri, M; Bovolenta, M; Martoni, E; Maraldi, Nm; Gualandi, F; Merlini, L; Ballestri, M; Tondelli, L; Sparnacci, K; Bonaldo, Paolo; Caputo, Antonella; Laus, M; Ferlini, A.
M.P.1.01 Pilot trial with cyclosporin A in patients with collagen VI myopathies
2009 L., Merlini; Angelin, Alessia; T., Tiepolo; Braghetta, Paola; P., Sabatelli; A., Zamparelli; A., Armaroli; M. E., Michelini; A., Ferlini; N. M., Maraldi
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