GRUMATI, PAOLO
GRUMATI, PAOLO
Dipartimento di Medicina Molecolare - DMM
Ambra1 deficiency impairs mitophagy in skeletal muscle
2022 Gambarotto, Lisa; Metti, Samuele; Chrisam, Martina; Cerqua, Cristina; Sabatelli, Patrizia; Armani, Andrea; Zanon, Carlo; Spizzotin, Marianna; Castagnaro, Silvia; Strappazzon, Flavie; Grumati, Paolo; Cescon, Matilde; Braghetta, Paola; Trevisson, Eva; Cecconi, Francesco; Bonaldo, Paolo
Aspartate metabolism in endothelial cells activates the mTORC1 pathway to initiate translation during angiogenesis
2022 Oberkersch, Roxana E; Pontarin, Giovanna; Astone, Matteo; Spizzotin, Marianna; Arslanbaeva, Liaisan; Tosi, Giovanni; Panieri, Emiliano; Ricciardi, Sara; Allega, Maria Francesca; Brossa, Alessia; Grumati, Paolo; Bussolati, Benedetta; Biffo, Stefano; Tardito, Saverio; Santoro, Massimo M
Autophagy activation in COL6 myopathic patients by a low-protein-diet pilot trial
2016 Castagnaro, Silvia; Pellegrini, Camilla; Pellegrini, Massimo; Chrisam, Martina; Sabatelli, Patrizia; Toni, Silvia; Grumati, Paolo; Ripamonti, Claudio; Pratelli, Loredana; Maraldi, Nadir M.; Cocchi, Daniela; Righi, Valeria; Faldini, Cesare; Sandri, Marco; Bonaldo, Paolo; Merlini, Luciano
Autophagy activation in COL6 myopathic patients by a low-protein-diet pilot trial
2016 Castagnaro, Silvia; Pellegrini, Chiara; Pellegrini, M; Chrisam, Martina; Sabatelli, P; Toni, Simona; Grumati, Paolo; Ripamonti, C; Pratelli, L; Maraldi, Nm; Cocchi, Davide; Righi, V; Faldini, C; Sandri, Marco; Bonaldo, Paolo; Merlini, Luigi
Autophagy in Skeletal Muscle Homeostasis and in Muscular Dystrophies
2012 Grumati, Paolo; Bonaldo, Paolo
Autophagy induction rescues muscular dystrophy
2011 Grumati, Paolo; Coletto, L; Sandri, Marco; Bonaldo, Paolo
Autophagy is defective in collagen VI muscular dystrophies, and its reactivation rescues myofiber degeneration.
2010 Grumati, Paolo; Coletto, L; Sabatelli, P; Cescon, Matilde; Angelin, Alessia; Bertaggia, Enrico; Blaauw, Bert; Urciuolo, Anna; Tiepolo, Tania; Merlini, L; Maraldi, Nm; Bernardi, Paolo; Sandri, Marco; Bonaldo, Paolo
Autophagy regulator and the uses thereof in the treatment of collagen VI defective Muscular Dystrophies
2010 Bonaldo, Paolo; Sandri, Marco; Grumati, Paolo; Coletto, L.
Autosomal recessive myosclerosis myopathy is a collagen VI disorder
2008 Merlini, L; Martoni, E; Grumati, Paolo; Sabatelli, P; Squarzoni, S; Urciuolo, Anna; Ferlini, A; Gualandi, F; Bonaldo, Paolo
Cardiac glycoside ouabain induces autophagic cell death in non-small cell lung cancer cells via a JNK-dependent decrease of Bcl-2
2014 Trenti, Annalisa; Grumati, Paolo; Cusinato, Federico; Orso, G; Bonaldo, Paolo; Trevisi, Lucia
Changes in Muscle Cell Metabolism and Mechanotransduction Are Associated with Myopathic Phenotype in a Mouse Model of Collagen VI Deficiency
2013 Sara De, Palma; Roberta, Leone; Grumati, Paolo; Michele, Vasso; Roman, Polishchuk; Daniele, Capitanio; Braghetta, Paola; Bernardi, Paolo; Bonaldo, Paolo; Cecilia, Gelfi
Collagen VI regulates satellite cell self-renewal and muscle regeneration
2013 Urciuolo, Anna; Quarta, M; Morbidoni, Valeria; Gattazzo, F; Molon, Sibilla; Grumati, Paolo; Montemurro, F; Tedesco, Fs; Blaauw, Bert; Cossu, G; Vozzi, G; Rando, Ta; Bonaldo, Paolo
Cyclosporine A in Ullrich congenital muscular dystrophy: long-term results.
2011 Merlini, L; Sabatelli, P; Armaroli, A; Gnudi, S; Angelin, Alessia; Grumati, Paolo; Michelini, Me; Franchella, A; Gualandi, F; Bertini, E; Maraldi, Nm; Ferlini, A; Bonaldo, Paolo; Bernardi, Paolo
Differential and restricted expression of novel collagen VI chains in mouse.
2011 Gara, Sk; Grumati, Paolo; Squarzoni, S; Sabatelli, P; Urciuolo, Anna; Bonaldo, Paolo; Paulsson, M; Wagener, R.
Expression of collagen VI α5 and α6 chains in human muscle and in Duchenne muscular dystrophy-related muscle fibrosis
2012 Patrizia, Sabatelli; Francesca, Gualandi; Sudheer Kumar, Gara; Grumati, Paolo; Alessandra, Zamparelli; Elena, Martoni; Camilla, Pellegrini; Luciano, Merlini; Alessandra, Ferlini; Bonaldo, Paolo; Nadir Mario, Maraldi; Mats, Paulsson; Stefano, Squarzoni; Raimund, Wagener
Expression of collagen VI α5 and α6 chains in human muscle and in Duchenne muscular dystrophy-related muscle fibrosis
2011 Sabatelli, P; Gualandi, F; Gara, Sk; Grumati, Paolo; Zamparelli, A; Martoni, E; Pellegrini, C; Merlini, L; Ferlini, A; Bonaldo, Paolo; Maraldi, Nm; Paulsson, M; Squarzoni, S; Wagener, R.
Expression of the Collagen VI a5 and a6 Chainsin Normal Human Skin and in Skin of Patientswith Collagen VI-Related Myopathies
2010 Sabatelli, P; Gara, Sk; Grumati, Paolo; Urciuolo, Anna; Gualandi, F; Curci, R; Squarzoni, S; Zamparelli, A; Martoni, E; Merlini, L; Paulsson, M; Bonaldo, Paolo; Wagener, R.
Extracellular collagen VI has prosurvival and autophagy instructive properties in mouse fibroblasts
2018 Castagnaro, Silvia; Chrisam, Martina; Cescon, Matilde; Braghetta, Paola; Grumati, Paolo; Bonaldo, Paolo
Identification and characterization of novel collagen VI non-canonical splicing mutations causing ullrich congenital muscular dystrophy.
2009 Martoni, E; Urciuolo, Anna; Sabatelli, P; Fabris, M; Bovolenta, M; Neri, M; Grumati, Paolo; D'Amico, A; Pane, M; Mercuri, E; Bertini, E; Merlini, L; Bonaldo, Paolo; Ferlini, A; Gualandi, F.
Identification of a deep intronic mutation in the COL6A2 gene by a novel custom oligonucleotide CGH array designed to explore allelic and genetic heterogeneity in collagen VI-related myopathies.
2010 Bovolenta, M; Neri, M; Martoni, E; Urciuolo, Anna; Sabatelli, P; Fabris, M; Grumati, Paolo; Mercuri, E; Bertini, E; Merlini, L; Bonaldo, Paolo; Ferlini, A; Gualandi, F.