Sfoglia per Autore
M.P.1.01 Pilot trial with cyclosporin A in patients with collagen VI myopathies
2009 L., Merlini; Angelin, Alessia; T., Tiepolo; Braghetta, Paola; P., Sabatelli; A., Zamparelli; A., Armaroli; M. E., Michelini; A., Ferlini; N. M., Maraldi
EM.P.5.03 The cyclophilin inhibitor Debio 025 normalizes mitochondrial function, muscle apoptosis and ultrastructural defects in Col6a1-/- myopathic mice
2009 Angelin, Alessia; T., Tiepolo; E., Palma; P., Sabatelli; L., Merlini; L., Nicolosi; F., Finetti; Braghetta, Paola; G., Vuagniaux; J. M., Dumont
Analysis of beta cell proliferation dynamics in zebrafish
2009 Moro, Enrico; Gnugge, L; Braghetta, Paola; Bortolussi, Marino; Argenton, Francesco
Lentiviral-mediated RNAi in vivo silencing of Col6a1, a gene with complex tissue specific expression pattern
2009 Frka, K.; Facchinello, N.; DEL VECCHIO, Claudia; Carpi, A.; Curtarello, M.; Venerando, R.; Angelin, Alessia; Parolin, MARIA CRISTINA; Bernardi, Paolo; Bonaldo, Paolo; Volpin, D.; Braghetta, Paola; Bressan, G. M.
The cyclophilin inhibitor Debio 025 normalizes mitochondrial function, muscle apoptosis and ultrastructural defects in Col6a1-/- myopathic mice
2009 Tiepolo, Tania; Angelin, Alessia; Palma, Elena; Sabatelli, P; Merlini, L; Nicolosi, L; Finetti, F; Braghetta, Paola; Vuagniaux, G; Dumont, Jm; Baldari, Ct; Bonaldo, Paolo; Bernardi, Paolo
S12.28 Rescue of myopathic collagen VI null mice by genetic inactivation of mitochondrial cyclophilin d
2008 E., Palma; E., Basso; Angelin, Alessia; T., Tiepolo; Braghetta, Paola; P., Sabatelli; N., Maraldi; M., Forte; Bonaldo, Paolo; Bernardi, Paolo
Tumor cell NG2 proteoglycan controls cancer progression through its interaction with host Collagen type VI
2008 P. A., Nicolosi; S., Cattaruzza; Braghetta, Paola; L., Pazzaglia; M. S., Benassi; N., Bertani; K., Lacrima; P., Picci; Bonaldo, Paolo; R., Perris
Expression pattern and function analysis of Emilin genes in zebrafish
2008 Milanetto, Martina; Tiso, Natascia; Braghetta, Paola; Volpin, Dino; Argenton, Francesco; Bonaldo, P.
The systemic administration of a low dose of 20MePS-AON combined with novel cationic polymethylmethacrylate nanoparticles induces the rescue of dystrophin expression in the mdx murine model
2008 Rimessi, P; Sabatelli, P; Fabris, M; Braghetta, Paola; Bassi, E; Spitali, P; Vattemi, G; Tomelleri, G; Mari, L; Perrone, D; Medici, A; Neri, M; Bovolenta, M; Martoni, E; Maraldi, N; Bonaldo, P; Gualandi, F; Merlini, L; Tondelli, L; Sparnacci, K; Caputo, Antonella; Laus, M; Ferlini, A.
Emilin genes are duplicated and dynamically expressed during zebrafish embryonic development
2008 Milanetto, Martina; Tiso, Natascia; Braghetta, Paola; Volpin, Dino; Argenton, Francesco; Bonaldo, Paolo
Cyclosporin A corrects mitochondrial dysfunction and muscle apoptosis in patients with collagen VI myopathies.
2008 Merlini, L; Angelin, Alessia; Tiepolo, Tania; Braghetta, Paola; Sabatelli, P; Zamparelli, A; Ferlini, A; Maraldi, Nm; Bonaldo, Paolo; Bernardi, Paolo
An enhancer required for transcription of the Col6a1 gene in muscle connective tissue is induced by signals released from muscle cells.
2008 Braghetta, Paola; Ferrari, A; Fabbro, C; Bizzotto, Dario; Volpin, Dino; Bonaldo, Paolo; Bressan, Giorgio
Emilin1 links TGF-beta maturation to blood pressure homeostasis
2006 Zacchigna, Luca; Vecchione, C.; Notte, A.; Cordenonsi, Michelangelo; Dupont, Sirio; Maretto, Silvia; Cifelli, G.; Ferrari, A.; Maffei, A.; Fabbro, Carla; Braghetta, Paola; Marino, G.; Selvetella, G.; Aretini, A.; Colonnese, C.; Bettarini, U.; Russo, G.; Soligo, SANDRA MARIA; Adorno, Maddalena; Bonaldo, Paolo; D., Volpin; Piccolo, Stefano; Lembo, G.; Bressan, Giorgio
COLLAGEN VI MYOPATHIES: FROM MOUSE THERAPY TO HUMAN TRIALS
2005 Paolo, Bonaldo; Natascha, Bergamin; Tiepolo, Tania; Paolo, Grumati; Braghetta, Paola; Bernardi, Paolo; Alessia, Angelin; Luca, Nicolosi; SORIANO GARCIA - CUERVA, MARIA EUGENIA; Valeria, Petronilli; Maraldi, NADIR M.; Patrizia, Sabatelli; Giovanna, Lattanzi; Elisabetta, Mattioli; Luciano, Merlini; Reggiani, Carlo; Megighian, Aram; Marta, Canato; Toniolo, Luana; Marco, Quarta
Analysis of regulatory regions of Emilin1 gene and their combinatorial contribution to tissue-specific transcription
2005 Fabbro, C.; DE GEMMIS, P.; Braghetta, Paola; Colombatti, A.; Volpin, Dino; Bonaldo, Paolo; Bressan, Giorgio
EMILIN-1 deficiency induces elastogenesis and vascular cell defects
2004 Zanetti, Miriam; Braghetta, Paola; Sabatelli, P.; Mura, I.; Doliana, R.; Colombatti, A.; Volpin, Dino; Bonaldo, Paolo; Bressan, Giorgio
Overlapping, complementary and site-specific expression pattern of genes of the EMILIN/Multimerin family
2004 Braghetta, Paola; Ferrari, A.; DE GEMMIS, P.; Zanetti, M.; Volpin, Dino; Bonaldo, Paolo; Bressan, Giorgio
Mapping Wnt/beta-catenin signaling during mouse development and in colorectal tumors.
2003 Maretto, S; Cordenonsi, Michelangelo; Dupont, Sirio; Braghetta, Paola; Broccoli, V; Hassan, Ab; Volpin, Dino; Bressan, Giorgio; Piccolo, Stefano
Mitochondrial dysfunction and apoptosis in myopathic mice with collagen VI deficiency
2003 Irwin, Wa; Bergamin, N; Sabatelli, P; Reggiani, Carlo; Megighian, Aram; Merlini, L; Braghetta, Paola; Columbaro, M; Volpin, Dino; Bressan, Giorgio; Bernardi, Paolo; Bonaldo, Paolo
Hmga2 promoter analysis in transgenic mice
2003 Schiltz, J. F.; Rustighi, A.; Tessari, M. A.; Liu, J.; Braghetta, Paola; Sgarra, R.; Stebel, M.; Bressan, Giorgio; Altruda, F.; Giancotti, V.; Chada, K.; Manfioletti, G.
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