CERUTTI, RAFFAELE

CERUTTI, RAFFAELE  

Dipartimento di Scienze Biomediche - DSB  

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Risultati 1 - 17 di 17 (tempo di esecuzione: 0.043 secondi).
Titolo Data di pubblicazione Autori Rivista Serie Titolo libro
A Single Intravenous Injection of AAV-PHP.B-hNDUFS4 Ameliorates the Phenotype of Ndufs4−/− Mice 2020 Cerutti R.Zeviani M.Viscomi C. + MOLECULAR THERAPY. METHODS & CLINICAL DEVELOPMENT - -
APOPT1/COA8 assists COX assembly and is oppositely regulated by UPS and ROS 2019 Cerutti, RaffaeleViscomi, CarloFernandez-Vizarra, ErikaZeviani, Massimo + EMBO MOLECULAR MEDICINE - -
Defective PITRM1 mitochondrial peptidase is associated with Aβ amyloidotic neurodegeneration 2016 Fernandez-Vizarra, ErikaCerutti, RaffaeleD'Amati, GiuliaViscomi, CarloZeviani, Massimo + EMBO MOLECULAR MEDICINE - -
Defective PITRM1 mitochondrial peptidase is associated with Aβ amyloidotic neurodegeneration 2016 Cerutti R.Viscomi C.Zeviani M. + EMBO MOLECULAR MEDICINE - -
DNA polymerase gamma mutations that impair holoenzyme stability cause catalytic subunit depletion 2021 Cerutti, RaffaeleZeviani, MassimoViscomi, Carlo + NUCLEIC ACIDS RESEARCH - -
Double administration of self-complementary AAV9(NDUFS4) prevents Leigh disease in Ndufs4(-/-) mice 2022 Cerutti, RViscomi, CZeviani, M + BRAIN - -
Genome editing in mitochondria corrects a pathogenic mtDNA mutation in vivo 2018 Viscomi C.Cerutti R.Zeviani M.Frezza C. + NATURE MEDICINE - -
In vivo correction of COX deficiency by activation of the AMPK/PGC-1α axis 2011 Viscomi C.Cerutti R.Zeviani M. + CELL METABOLISM - -
Mouse models for the study of mitochondrial disorders 2024 CERUTTI, RAFFAELE - - -
NAD+-dependent activation of Sirt1 corrects the phenotype in a mouse model of mitochondrial disease 2014 Cerutti R.Viscomi C.Zeviani M. + CELL METABOLISM - -
Opa1 Overexpression Protects from Early-Onset Mpv17−/−-Related Mouse Kidney Disease 2020 Cerutti R.Scorrano L.Zeviani M.Viscomi C. + MOLECULAR THERAPY - -
Perturbed Redox Signaling Exacerbates a Mitochondrial Myopathy 2018 Cerutti R.Zeviani M.Viscomi C. + CELL METABOLISM - -
Rapamycin rescues mitochondrial myopathy via coordinated activation of autophagy and lysosomal biogenesis 2018 Cerutti R.Viscomi C.Zeviani M. + EMBO MOLECULAR MEDICINE - -
SURF1 knockout cloned pigs: Early onset of a severe lethal phenotype 2018 Cerutti, RFernandez-Vizarra, ErikaViscomi, CZeviani, M + BIOCHIMICA ET BIOPHYSICA ACTA. MOLECULAR BASIS OF DISEASE - -
The ferredoxin-NADP+ reductase/ferredoxin electron transfer system of Plasmodium falciparum 2009 Cerutti R. + THE FEBS JOURNAL - -
TTC19 Plays a Husbandry Role on UQCRFS1 Turnover in the Biogenesis of Mitochondrial Respiratory Complex III 2017 Cerutti, RaffaeleD'Amati, GiuliaViscomi, CarloFernandez-Vizarra, ErikaZeviani, Massimo + MOLECULAR CELL - -
TTC19 Plays a Husbandry Role on UQCRFS1 Turnover in the Biogenesis of Mitochondrial Respiratory Complex III 2017 Cerutti R.Viscomi C.Zeviani M. + MOLECULAR CELL - -