CERUTTI, RAFFAELE
CERUTTI, RAFFAELE
Università di Padova
APOPT1/COA8 assists COX assembly and is oppositely regulated by UPS and ROS
2019 Signes, Alba; Cerutti, Raffaele; Dickson, Anna S; Benincá, Cristiane; Hinchy, Elizabeth C; Ghezzi, Daniele; Carrozzo, Rosalba; Bertini, Enrico; Murphy, Michael P; Nathan, James A; Viscomi, Carlo; Fernandez-Vizarra, Erika; Zeviani, Massimo
Defective PITRM1 mitochondrial peptidase is associated with Aβ amyloidotic neurodegeneration
2016 Brunetti, Dario; Torsvik, Janniche; Dallabona, Cristina; Teixeira, Pedro; Sztromwasser, Pawel; Fernandez-Vizarra, Erika; Cerutti, Raffaele; Reyes, Aurelio; Preziuso, Carmela; D'Amati, Giulia; Baruffini, Enrico; Goffrini, Paola; Viscomi, Carlo; Ferrero, Ileana; Boman, Helge; Telstad, Wenche; Johansson, Stefan; Glaser, Elzbieta; Knappskog, Per M; Zeviani, Massimo; Bindoff, Laurence A
DNA polymerase gamma mutations that impair holoenzyme stability cause catalytic subunit depletion
2021 Silva-Pinheiro, Pedro; Pardo-Hernández, Carlos; Reyes, Aurelio; Tilokani, Lisa; Mishra, Anup; Cerutti, Raffaele; Li, Shuaifeng; Rozsivalova, Dieu-Hien; Valenzuela, Sebastian; Dogan, Sukru A; Peter, Bradley; Fernández-Silva, Patricio; Trifunovic, Aleksandra; Prudent, Julien; Minczuk, Michal; Bindoff, Laurence; Macao, Bertil; Zeviani, Massimo; Falkenberg, Maria; Viscomi, Carlo
Double administration of self-complementary AAV9(NDUFS4) prevents Leigh disease in Ndufs4(-/-) mice
2022 Corra, S; Cerutti, R; Balmaceda, V; Viscomi, C; Zeviani, M
Opa1 Overexpression Protects from Early-Onset Mpv17−/−-Related Mouse Kidney Disease
2020 Luna-Sanchez, M.; Beninca, C.; Cerutti, R.; Brea-Calvo, G.; Yeates, A.; Scorrano, L.; Zeviani, M.; Viscomi, C.
SURF1 knockout cloned pigs: Early onset of a severe lethal phenotype
2018 Quadalti, C; Brunetti, D; Lagutina, I; Duchi, R; Perota, A; Lazzari, G; Cerutti, R; Di Meo, I; Johnson, M; Bottani, E; Crociara, P; Corona, C; Grifoni, S; Tiranti, V; Fernandez-Vizarra, Erika; Robinson, A J; Viscomi, C; Casalone, C; Zeviani, M; Galli, C
TTC19 Plays a Husbandry Role on UQCRFS1 Turnover in the Biogenesis of Mitochondrial Respiratory Complex III
2017 Bottani, Emanuela; Cerutti, Raffaele; Harbour, Michael E; Ravaglia, Sabrina; Dogan, Sukru Anil; Giordano, Carla; Fearnley, Ian M; D'Amati, Giulia; Viscomi, Carlo; Fernandez-Vizarra, Erika; Zeviani, Massimo