Sfoglia per Autore
Mitochondrial DNA heteroplasmy is modulated during oocyte development propagating mutation transmission
2021 Zhang, Han; Esposito, M.; Pezet, M. G.; Aryaman, J.; Wei, Wei; Klimm, F.; Calabrese, C.; Burr, S. P.; Macabelli, C. H.; Viscomi, C.; Saitou, M.; Chiaratti, M. R.; Stewart, J. B.; Jones, N.; Chinnery, P. F.
Structural basis for a complex I mutation that blocks pathological ROS production
2021 Yin, Z.; Burger, N.; Kula-Alwar, D.; Aksentijevic, D.; Bridges, H. R.; Prag, H. A.; Grba, D. N.; Viscomi, C.; James, A. M.; Mottahedin, A.; Krieg, T.; Murphy, M. P.; Hirst, J.
Role of pitrm1 in mitochondrial dysfunction and neurodegeneration
2021 Brunetti, D.; Catania, A.; Viscomi, C.; Deleidi, M.; Bindoff, L. A.; Ghezzi, D.; Zeviani, M.
DNA polymerase gamma mutations that impair holoenzyme stability cause catalytic subunit depletion
2021 Silva-Pinheiro, Pedro; Pardo-Hernández, Carlos; Reyes, Aurelio; Tilokani, Lisa; Mishra, Anup; Cerutti, Raffaele; Li, Shuaifeng; Rozsivalova, Dieu-Hien; Valenzuela, Sebastian; Dogan, Sukru A; Peter, Bradley; Fernández-Silva, Patricio; Trifunovic, Aleksandra; Prudent, Julien; Minczuk, Michal; Bindoff, Laurence; Macao, Bertil; Zeviani, Massimo; Falkenberg, Maria; Viscomi, Carlo
Exploiting pyocyanin to treat mitochondrial disease due to respiratory complex III dysfunction
2021 Peruzzo, Roberta; Corrà, Samantha; Costa, Roberto; Brischigliaro, Michele; Varanita, Tatiana; Biasutto, Lucia; Rampazzo, Chiara; Ghezzi, Daniele; Leanza, Luigi; Zoratti, Mario; Zeviani, Massimo; De Pittà, Cristiano; Viscomi, Carlo; Costa, Rodolfo; Szabò, Ildikò
Respiratory chain signalling is essential for adaptive remodelling following cardiac ischaemia
2020 Szibor, M.; Schreckenberg, R.; Gizatullina, Z.; Dufour, E.; Wiesnet, M.; Dhandapani, P. K.; Debska-Vielhaber, G.; Heidler, J.; Wittig, I.; Nyman, T. A.; Gartner, U.; Hall, A. R.; Pell, V.; Viscomi, C.; Krieg, T.; Murphy, M. P.; Braun, T.; Gellerich, F. N.; Schluter, K. -D.; Jacobs, H. T.
Opa1 Overexpression Protects from Early-Onset Mpv17−/−-Related Mouse Kidney Disease
2020 Luna-Sanchez, M.; Beninca, C.; Cerutti, R.; Brea-Calvo, G.; Yeates, A.; Scorrano, L.; Zeviani, M.; Viscomi, C.
A Single Intravenous Injection of AAV-PHP.B-hNDUFS4 Ameliorates the Phenotype of Ndufs4−/− Mice
2020 Silva-Pinheiro, P.; Cerutti, R.; Luna-Sanchez, M.; Zeviani, M.; Viscomi, C.
Loss of function of the mitochondrial peptidase PITRM1 induces proteotoxic stress and Alzheimer’s disease-like pathology in human cerebral organoids
2020 Perez, M. J.; Ivanyuk, D.; Panagiotakopoulou, V.; Di Napoli, G.; Kalb, S.; Brunetti, D.; Al-Shaana, R.; Kaeser, S. A.; Fraschka, S. A. -K.; Jucker, M.; Zeviani, M.; Viscomi, C.; Deleidi, M.
Metabolic effects of bezafibrate in mitochondrial disease
2020 Steele, H; Gomez-Duran, A; Pyle, A; Hopton, S; Newman, J; Stefanetti, Rj; Charman, Sj; Parikh, Jd; He, Lp; Viscomi, C; Jakovljevic, Dg; Hollingsworth, Kg; Robinson, Aj; Taylor, Rw; Bottolo, L; Horvath, R; Chinnery, Pf
Strategies for fighting mitochondrial diseases
2020 Viscomi, Carlo; Zeviani, Massimo
Bioenergetic consequences from xenotopic expression of a tunicate AOX in mouse mitochondria: Switch from RET and ROS to FET
2020 Szibor, Marten; Gainutdinov, Timur; Fernandez-Vizarra, Erika; Dufour, Eric; Gizatullina, Zemfira; Debska-Vielhaber, Grazyna; Heidler, Juliana; Wittig, Ilka; Viscomi, Carlo; Gellerich, Frank; Moore, Anthony L
Bioenergetic consequences from xenotopic expression of a tunicate AOX in mouse mitochondria: Switch from RET and ROS to FET
2020 Szibor, M.; Gainutdinov, T.; Fernandez-Vizarra, E.; Dufour, E.; Gizatullina, Z.; Debska-Vielhaber, G.; Heidler, J.; Wittig, I.; Viscomi, C.; Gellerich, F.; Moore, A. L.
Breathe: Your Mitochondria Will Do the Rest… If They Are Healthy!
2019 Viscomi, C.; Zeviani, M.
The homeostatic dynamics of feeding behaviour identify novel mechanisms of anorectic agents
2019 Mcgrath, T. M.; Spreckley, E.; Rodriguez, A. F.; Viscomi, C.; Alamshah, A.; Akalestou, E.; Murphy, K. G.; Jones, N. S.
Erratum: Control of mitochondrial superoxide production by reverse electron transport at complex I. (Journal of Biological Chemistry 2018 293 (9869–9879) DOI: 10.1074/jbc.RA118.003647)
2019 Robb, E. L.; Hall, A. R.; Prime, T. A.; Eaton, S.; Szibor, M.; Viscomi, C.; James, A. M.; Murphy, MICHAEL PATRICK
Niche stiffness underlies the ageing of central nervous system progenitor cells
2019 Segel, M.; Neumann, B.; Hill, M. F. E.; Weber, I. P.; Viscomi, C.; Zhao, C.; Young, A.; Agley, C. C.; Thompson, A. J.; Gonzalez, G. A.; Sharma, A.; Holmqvist, S.; Rowitch, D. H.; Franze, K.; Franklin, R. J. M.; Chalut, K. J.
Physical and Functional Cross Talk Between Endo-Sarcoplasmic Reticulum and Mitochondria in Skeletal Muscle
2019 Boncompagni, Simona; Pozzer, Diego; Viscomi, Carlo; Ferreiro, Ana; Zito, Ester
APOPT1/COA8 assists COX assembly and is oppositely regulated by UPS and ROS
2019 Signes, A.; Cerutti, R.; Dickson, A. S.; Beninca, C.; Hinchy, E. C.; Ghezzi, D.; Carrozzo, R.; Bertini, E.; Murphy, M. P.; Nathan, J. A.; Viscomi, C.; Fernandez-Vizarra, E.; Zeviani, M.
APOPT1/COA8 assists COX assembly and is oppositely regulated by UPS and ROS
2019 Signes, Alba; Cerutti, Raffaele; Dickson, Anna S; Benincá, Cristiane; Hinchy, Elizabeth C; Ghezzi, Daniele; Carrozzo, Rosalba; Bertini, Enrico; Murphy, Michael P; Nathan, James A; Viscomi, Carlo; Fernandez-Vizarra, Erika; Zeviani, Massimo
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