VERGANI, LODOVICA
VERGANI, LODOVICA
Carnitine deficiency induced during hemodialysis and hyperlipidemia: Effect of replacement therapy
1981 Bertoli, M.; Battistella, P. A.; Vergani, L.; Naso, A.; Gasparotto, M. L.; Romagnoli, G. F.; Angelini, C.
Childhood encephalomyopathy with cytochrome c oxidase deficiency, ataxia, muscle wasting, and mental impairment
1986 Angelini, C.; Bresolin, N.; Pegolo, G.; Bet, L.; Rinaldo, P.; Trevisan, C.; Vergani, L.
Clinical varieties of carnitine and carnitine palmitoyltransferase deficiency
1987 Angelini, C.; Trevisan, C.; Isaya, G.; Pegolo, G.; Vergani, L.
Clinical varieties of carnitine and carnitine palmitoyltransferase deficiency
1987 Angelini, C.; Trevisan, C.; Isaya, G.; Pegolo, G.; Vergani, L.
Hypertrophic cardiomyopathy with mitochondrial myopathy. A new phenotype of complex II defect.
1993 Angelini, Corrado; Melacini, Paola; Valente, Marialuisa; Reichmann, H; Carrozzo, R; Fanin, Marina; Vergani, Lodovica; Boffa, Giovanni; Martinuzzi, A; Fasoli, Giuseppe
Physiological responses in McArdle's patients during maximal aerobic exercise
1993 Martinuzzi, A; Pegoraro, Elena; Cadaldini, M; Schiraldi, C; Costa, A; Vergani, Lodovica; Angelini, Corrado
Hereditary protein C deficiency associated with riboflavin-responsive lipid storage myopathy
1996 Vergani, Lodovica; Angelini, Corrado; Pegoraro, Elena; Cadaldini, M; Simioni, Paolo; Girolami, Antonio; Turnbull, Dm
Diagnosis and therapy of myophosphorylase deficiency: experience with a group of italian patients
1996 Martinuzzi, A; Schievano, G; Vergani, Lodovica; Fanin, Marina; Pegoraro, Elena; Schiraldi, C; Vita, G; Siciliano, G; Toscano, A; Angelini, Corrado
Riboflovin responsive myopathy: correlation between mitochondrial oxidative phosphorilation enzymes and mitochondrial flavocoenzyme homeostasis.
1999 Vergani, Lodovica; Barile, M.; Angelini, C.; Burlina, A. B.; Nijmtans, L.; Brizio, C.; Zerbetto, E.; DABBENI SALA, Federica
Alteration of mechanisms responsible for the homeostasis of mitochondrial flavin cofactors are correlated with adult lipid storage myopathies
1999 Vergani, Lodovica; Barile, M; Angelini, C; BURLINA A., B; Nijmtans, L; FREDA M., P; Brizio, C; Zerbetto, E; DABBENI SALA, Federica
Riboflavin therapy. Biochemical heterogeneity in two adult lipid storage myopathies.
1999 Vergani, Lodovica; Barile, M; Angelini, Corrado; BURLINA A., B; Nijtmans, L; FREDA M., P; Brizio, C; Zerbetto, E; DABBENI SALA, Federica
Energy status and ROS production in three RHO0 cell lines with different nuclear background
2001 Vergani, Lodovica; Floreani, Maura; Ceccon, M.; Napoli, E.; Bufano, D.; Valente, L.; Holt, L.; DABBENI SALA, Federica
Antioxidant capacity in cybrids harbouring the three mtDNA mutations primarly associated with Leber’s (LHON)
2001 Napoli, E.; DABBENI SALA, Federica; Floreani, M.; Vergani, Lodovica; Valente, L.; Carelli, V.; Martinuzzi, A.
ANTIOXIDANT CAPACITY IN CYBRIDS HARBORING THE THREE MTDNA RELATED TO COMPLEX I MUTATIONS SUBUNITS AND PRIMARILY ASSOCIATED WITH LEBER'S (LHON)
2002 DABBENI SALA, Federica; Napoli, E.; Floreali, M.; Valente, L.; Vergani, Lodovica; Carelli, V.; Martinuzzi, A.
Biased incorporation of ribonucleotides on the mitochondrial L-strand accounts for apparent strand-asymmetric DNA replication.
2002 Yang, My; Bowmaker, M; Reyes, A; Vergani, Lodovica; Angeli, Paolo; Gringeri, Enrico; Jacobs, Ht; Holt, Ij
ROS HOMEOSTASIS AND ENERGY STATUS IN mtDNA DEPLETION
2003 Vergani, Lodovica; Ceccon, M.; Napoli, E.; Valente, L.; Bragantini, F.; Floreani, Maura; Holt, I. J.; DABBENI SALA, Federica
Decreased fatty-acid beta-oxidation in riboflavin-responsive, multiple acylcoenzyme A dehydrogenase-deficient patients is associated with an increase in uncoupling protein-3
2003 Russell, Ap; Schrauwen, P; Somm, E; Gastaldi, G; Hesselink, Mk; Schaart, G; Kornips, E; Lo, Sk; Bufano, D; Giacobino, Jp; Muzzin, P; Ceccon, M; Angelini, Corrado; Vergani, Lodovica
Homeostasis of reactive oxygen species in mtDNA-depleted cell lines
2003 Vergani, Lodovica; Ceccon, M.; Napoli, E.; Valente, L.; Cabrelle, A.; Bragantini, F.; Floreani, Maura; DABBENI SALA, Federica
Abnormal free radical homeostasis and oxphos activity in ALS muscle
2003 Soraru', Gianni; Vergani, Lodovica; D'Ascenzo, C.; Fedrizzi, Laura; Angelini, Corrado
Antioxidant defences and reactive oxygen species homeostasis in different human mitochondrial DNA-depleted cell lines.
2004 Vergani, Lodovica; Floreani, Maura; Russell, A.; Ceccon, M.; Napoli, E.; Cabrelle, A.; Valente, L.; Bragantini, F.; Leger, B.; DABBENI SALA, Federica