SANDONA', DORIANNA
SANDONA', DORIANNA
Dipartimento di Scienze Biomediche - DSB
1st International Workshop on Clinical trial readiness for sarcoglycanopathies 15-16 November 2016, Evry, France
2017 Marsolier, Justine; Laforet, Pascal; Pegoraro, Elena; Vissing, John; Richard, Isabelle; Barnerias, Christine; Carlier, Robert Yves; Díaz Manera, Jordi; Fayssoil, Abdallah; Galy, Anne; Gazzerro, Elisabetta; Gorecki, DARIUSZ , CEZARY; Guglieri, Michela; Hogrel, Jean Yves; Israeli, David; Leturcq, France; Moussu, Helene; Prigent, Helene; Sandona', Dorianna; Schoser, Benedikt; Semplicini, Claudio; Talim, Beril; Tasca, Giorgio; Urtizberea, Andoni; Udd, Bjarne
A single cell complementation class is common to several cases of Cytochrome c Oxidase defective Leigh's syndrome
1997 Munaro, M; Tiranti, V; Sandona', Dorianna; Lamantea, E; Uziel, G; Bisson, R; Zeviani, M.
A single point mutation (E166Q) prevents dicyclohexylcarbodiimide binding to the photosystem II subunit CP29
1997 Pesaresi, P; Sandona', Dorianna; Giuffra, E; Bassi, R.
A STRUCTURAL INVESTIGATION OF THE CENTRAL CHLOROPHYLL A BINDING SITES IN THE MINOR PHOTOSYSTEM II ANTENNA PROTEIN, LHCB4
2002 Pascal, A; Caffarri, S; Croce, R; Sandona', Dorianna; Bassi, R; Robert, B.
Adaptation of Mouse Skeletal Muscle to Long-Term Microgravity in the MDS Mission
2012 Sandona', Dorianna; Desaphy, Jf; Camerino, Gm; Bianchini, Elisa; Ciciliot, Stefano; Danieli, Daniela; Dobrowolny, G; Furlan, S; Germinario, Elena; Goto, K; Gutsmann, M; Kawano, F; Nakai, N; Ohira, T; Picard, ANNE ALEIDA; Salanova, M; Schiffl, G; Blottner, D; Musarò, A; Ohira, Y; Betto, R; Conte, D; Schiaffino, S.
An Automated Low-Cost Swim Tunnel for Measuring Swimming Performance in Fish
2021 Lucon-Xiccato, T.; Bella, L.; Mainardi, E.; Baraldi, M.; Bottarelli, M.; Sandona, D.; Bertolucci, C.
Analysis of some optical properties of a native and reconstituted photosystem II antenna complex, CP29: Pigment binding sites can be occupied by chlorophyll a or chlorophyll b and determine spectral forms
1997 Giuffra, E; Zucchelli, G; Sandona', Dorianna; Croce, R; Cugini, D; Garlaschi, Fm; Bassi, R; Jennings, Rc
Biological markers of oxidative stress in mitochondrial myopathies with progressive external ophthalmoplegia.
1991 Piccolo, G; Banfi, P; Azan, G; Rizzuto, Rosario; Bisson, R; Sandona', Dorianna; Bellomo, G.
Calcium overload of dystrophic muscle may depend on the high expression level of P2X7 receptor
2001 Betto, R; Sandona', Dorianna; Tarricone, Elena; Martinello, Tiziana; Morbiato, L; Biral, D.
CFTR corrector C17 is effective in muscular dystrophy, in vivo proof of concept in LGMDR3
2022 Scano, Martina; Benetollo, Alberto; Nogara, Leonardo; Bondi', Michela; DALLA BARBA, Francesco; Soardi, Michela; Sandra, Furlan; Akyurek, EYLEM EMEK; Caccin, Paola; Carotti, Marcello; Sacchetto, Roberta; Blaauw, Bert; Sandona', Dorianna
Characterization of a cDNA encoding subunit VI of cytochrome c oxidase from the slime mold Dictyostelium discoideum.
1991 Rizzuto, Rosario; Sandona', Dorianna; Capaldi, Ra; Bisson, R.
Characterization of the ATP-hydrolysing activity of alpha-sarcoglycan
2004 Sandona', Dorianna; Gastaldello, S; Martinello, Tiziana; Betto, R.
Chlorophyll binding to monomeric light-harvesting complex - A mutation analysis of chromophore-binding residues
1999 Remelli, R; Varotto, C; Sandona', Dorianna; Croce, R; Bassi, R.
Clinical, morphological and molecular genetic studies in patients with progressive xternal ophthalmoplegia and mitochondrial myopathy
1992 Piccolo, G; Azan, G; Banfi, P; Sandona', Dorianna; Brini, Marisa; Bisson, R; Rizzuto, Rosario
Combined Use of CFTR Correctors in LGMD2D Myotubes Improves Sarcoglycan Complex Recovery
2020 Carotti, Marcello; Scano, Martina; Fancello, Irene; Richard, Isabelle; Risato, Giovanni; Bensalah, Mona; Soardi, Michela; Sandona', Dorianna
Cultured adult muscle fibers in the microgravity environment. The MYO experiment in the Foton-M3 space flight mission
2009 Franzoso, S; Sandona', Dorianna; Picard, ANNE ALEIDA; Furlan, S; Gobbo, V; Salvatori, Sergio; Elvassore, Nicola; Cimetta, Elisa; Betto, R; Schiaffino, S.
Customized bioreactor enables the production of 3D diaphragmatic constructs influencing matrix remodeling and fibroblast overgrowth
2022 Maghin, E.; Carraro, E.; Boso, D.; Dedja, A.; Giagante, M.; Caccin, P.; Barna, R. A. -M.; Bresolin, S.; Cani, A.; Borile, G.; Sandrin, D.; Romanato, F.; Cecchinato, F.; Urciuolo, A.; Sandona, D.; De Coppi, P.; Pavan, P. G.; Piccoli, M.
Deficiency of alpha-sarcoglycan differently affects fast- and slow-twitch skeletal muscles
2005 Danieli, Daniela; Esposito, A; Germinario, Elena; Sandona', Dorianna; Martinello, Tiziana; JAKUBIEC PUKA, A; Biral, D; Betto, R.
Different outcome of sarcoglycan missense mutation between human and mouse
2018 Henriques, Sara F.; Patissier, Cécile; Bourg, Nathalie; Fecchio, Chiara; Sandona, Doriana; Marsolier, Justine; Richard, Isabelle
Differential Analysis of Gly211Val and Gly286Val Mutations Affecting Sarco(endo)plasmic Reticulum Ca2+-ATPase (SERCA1) in Congenital Pseudomyotonia Romagnola Cattle
2022 Akyurek, Eylem Emek; Busato, Francesca; Murgiano, Leonardo; Bianchini, Elisa; Carotti, Marcello; Sandonà, Dorianna; Drögemüller, Cord; Gentile, Arcangelo; Sacchetto, Roberta